ྑᐊ⫧
ྑᡣ
ྑᐊ
ᕥᐊ ᕥᡣ
⫵ື⬦
⫵⾑ὶῶᑡ
ࢳࣀ࣮ࢮ ࠶ࡾ
䝣䜯䝻−ᅄᚩ
ᚰᐊ୰㝸Ḟᦆ㛢㙐⾡
䠇
ྑᐊὶฟ㊰ᙧᡂ⾡
э㻌 ྑᐊὶฟ㊰㻌 ⊃✽䠇㏫ὶ
ᚰᐊ୰㝸Ḟᦆ
⫵ື⬦⊃✽
ື⬦㥽
ᑵᏛ࣭ᑵປ
ᏛṔ㸸㧗ᰯ ᬑ㏻Ꮫ⣭ࢆ༞ᴗࠊ㐍Ꮫࡏࡎࠋ
ᑵ⫋㸸ࣝࣂࢺࡢ⤒㦂ࡣ࠶ࡿࡀࠊ⥅⥆࡛ࡁࡎࠋ ⤥㸸࡞ࡋ㹼ᐃ
♫ಖ㞀
㌟య㞀ᐖ⪅ᡭᖒ㸸 㸱⣭
⒪⫱ᡭᖒ 㸸 ࡞ࡋ㸦▱ⓗ㞀ᐖ࡞ࡋ㸧 㔜ᗘᚰ㌟㞀ᐖ⪅་⒪㈝ຓᡂไᗘ㸸 ࡞ࡋ ་⒪㈝㸸 ᭷ᩱ
㞀ᐖᇶ♏ᖺ㔠 㸸 㸰⣭
⌧≧
ᚰᶵ⬟Ᏻᐃ
⫵ື⬦ᘚ⨨⾡ᚋࠊᑵ⫋ᕼᮃ ᑵປᨭ
Department of Pediatric Cardiology, Children‘s Medical Center, Ehime University Hospital
䠏䠑ṓ㻌 ⏨ᛶ䚸䝣䜯䝻䞊ᅄᚩ⾡ᚋ
㸯⣭
࡞ࡋ
࠶ࡾ
↓ᩱ
㸯⣭
⏕ά䜢ᨭ䛘䜛♫ಖ㞀ไᗘ䠄♫⚟♴䠅㻌 㻌
ᖺ㱋㻌㻌 ㄌ⏕㻌
䠄䠌ṓ䠅㻌㻌ᑵᏛ๓㻌㻌 ᑵᏛᮇ㻌 䠄䠒ṓ䡚㻝㻤ṓ䠅㻌㻌
Ꮚ⫱䛶䞉ᑵປᮇ㻌
䠄㻞㻜ṓ䡚㻌 㻠㻜ṓ㻌 㻢㻜ṓ㻌 ㏥⫋ᚋ㻌 䠄㻢㻡ṓ䡚㻌 㻣㻜ṓ䡚㻌
㻌 㻌 ಖ⫱ᡤ㻌㻌㻌 㻌 ㆤಖ㝤㻌 㻌 㻌 㻌 㻌
㻌 㻌 ẕᏊᐙᗞ➼᪥ᖖ⏕άᨭᴗ㻌㻌 㧗㱋⪅⚟♴㻌
㻌 㻌 㔛ぶጤク㻌 㻌 㻌㻌㻌 㻌 㣴ㆤ⪁ே䝩䞊䝮㻌 㻌 㻌
㻌 㻌 ඣ❺㣴ㆤタ㻌㻌㻌 㻌㻌㻌 㻌
㻌 㻌 ⒪⫱ᡭᖒ㻌㻌 㻌㻌㞀ᐖ⪅⮬❧ᨭἲ䛻䜘䜛㻌 㻌 㻌 㻌 㻌 㻌 㻌
㻌 㻌 ⢭⚄㞀ᐖ⪅ಖ⚟♴ᡭᖒ㻌 㻌 ྛ✀䝃䞊䝡䝇䛾⏝㻌 㻌 㻌
㻌 㻌 ㌟య㞀ᐖ⪅ᡭᖒ㻌䠄⮬❧ᨭ⤥䞉ᆅᇦ⏕άᨭᴗ䠅㻌 㻌 㻌 㻌 㻌
♫
⚟
♴ 同 呎 吪吐
ྛ✀䛾᭦⏕ㆤ䜢ཷ䛡䜛䛯䜑䛾๓ᥦ䛸䛺䜛䚹
㻌 ⏕ά䜢ᨭ䛘䜛♫ಖ㞀ไᗘ䠄ಖ䞉་⒪䠅㻌 㻌
ᖺ㱋㻌㻌 㻌 㻌 ㄌ⏕䠄䠌ṓ䠅㻌 ᑵᏛ๓㻌 ᑵᏛᮇ㻌 䠄䠒ṓ䡚㻝㻤ṓ䠅㻌㻌
Ꮚ⫱䛶䞉ᑵປ ᮇ䠄㻞㻜ṓ䡚㻌
㻠㻜 ṓ ṓ㻌
㏥⫋ᚋ㻌 䠄㻢㻡ṓ䡚㻌
㻣㻜ṓ䡚㻌 㻌 㻌 ẕᏊ
ᗣ ᡭᖒ㻌
ᐙᗞゼၥ㻌 ஙᗂඣデ㻌㻌 㻌 㻌
㻌 㻌 ᮍ⇍ඣ㣴⫱་⒪㈝ຓᡂ㻌 㻌 㻌
㻌 㻌 㻌 㻌 㻌 ண㜵᥋✀㻌 Ꮫᰯಖ㻌 デᴗ䠄⪁ேಖ䠅
ᗣᡭᖒ㻌 㻌 㻌
㻌 㻌 㻌 㻌 ஙᗂඣ་⒪㈝ຓᡂ㻌 㻌 㻌
㻌 㻌 㻌 㻌 ẕᏊᐙᗞ་⒪㈝ຓᡂ㻌 㻌 㻌 㻌 㻌
㻌 㻌 㻌 㻌 㔜ᗘᚰ㌟㞀ᐖ⪅་⒪㈝ຓᡂ㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌
㻌 㻌 ་⒪ಖ䠄ᅜẸᗣಖ㝤䞉♫ಖ㝤䞉ྛ✀ඹ῭䞉⯪ဨ䛺䛹䠅㻌㻌 㻌 ㏥⫋⪅་⒪㻌㻌 ⪁ேಖ་⒪㻌㻌
㻌 㻌 㻌 㻌 ᑠඣ៏ᛶ≉ᐃᝈ⒪◊✲ᴗ㻌 ≉ᐃᝈ⒪◊✲ᴗ㻌 㻌 㻌
㻌 㻌 㻌 㻌 ⮬❧ᨭ་⒪䠄⫱ᡂ་⒪䠅㻌 ⮬❧ᨭ་⒪䠄᭦⏕་⒪䠅㻌 㻌 㻌
㻌 㻌 㻌 㻌 ⮬❧ᨭ་⒪䠄⢭⚄㏻㝔་⒪䠅㻌 㻌 㻌 㻌 㻌
㻌 㻌 㻌 㻌 㧗㢠⒪㣴㈝䚸㧗㢠་⒪㈝ไᗘ㻌㻌 䊻ᶆ‽㈇ᢸ㝈ᗘ㢠ㄆᐃド䠄ධ㝔䛾䜏䠅㻌㻌
ಖ
䞉
་
⒪ ಖ 㞀㻌
㧗㢠་⒪㈝ไᗘ㻌 㻌
་⒪㈝㻌 100
㻌 㻌 㻌 㻌 㻌 э㻌 ❆ཱྀ䛷䛾㈇ᢸ䠄3䠅䛜䚸30䛛䛛䜛ሙྜ
212,570䜢㧗㢠⒪㣴㈝䛸䛧䛶ᨭ⤥䛧䚸ᐇ㝿䛾⮬ᕫ㈇ᢸ㢠䛿䚸87,430䚹 䊻㻌 ⮬ᕫ㈇ᢸ㝈ᗘ㢠㐺⏝ㄆᐃド㻌
㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 ᖹᡂ㻞㻠ᖺ㻠᭶䡚㻌 እ᮶䜒ྍ㻌
㧗㢠་⒪㈝ไᗘ㻌 㻌
㧗㢠་⒪䞉㧗㢠ㆤྜ⟬⒪㣴㈝ไᗘ㻌
㻌 㧗㢠⒪㣴㈝ไᗘ䛜䛂᭶䛃༢䛷㈇ᢸ䜢㍍ῶ䛩䜛䛾䛻ᑐ䛧䚸ྜ⟬㻌 㻌 ⒪㣴㈝ไᗘ䛿䚸䛣䛖䛧䛯䛂᭶䛃༢䛷䛾㈇ᢸ㍍ῶ䛜䛒䛳䛶䜒䚸䛺䛚㻌 㻌 㻌 㔜䛔㈇ᢸ䛜ṧ䜛ሙྜ䛻䛂ᖺ䛃༢䛷䛭䜜䜙䛾㈇ᢸ䜢㍍ῶ䛩䜛ไᗘ㻌 㻌
་⒪㈝᥍㝖ไᗘ㻌
㻌 ୍ᐃ䛾㔠㢠䛾ᡤᚓ᥍㝖䛾䛣䛸㻌
䠄䠐ᅇ┠䛛䜙䠅
㻌 ⏕ά䜢ᨭ䛘䜛♫ಖ㞀ไᗘ䠄ಖ䞉་⒪䠅㻌 㻌
ᖺ㱋㻌㻌 㻌 㻌 ㄌ⏕䠄䠌ṓ䠅㻌 ᑵᏛ๓㻌 ᑵᏛᮇ㻌 䠄䠒ṓ䡚㻝㻤ṓ䠅㻌㻌
Ꮚ⫱䛶䞉ᑵປ ᮇ䠄㻞㻜ṓ䡚㻌
㻠㻜 ṓ ṓ㻌
㏥⫋ᚋ㻌 䠄㻢㻡ṓ䡚㻌
㻣㻜ṓ䡚㻌 㻌 㻌 ẕᏊ
ᗣ ᡭᖒ㻌
ᐙᗞゼၥ㻌 ஙᗂඣデ㻌㻌 㻌 㻌
㻌 㻌 ᮍ⇍ඣ㣴⫱་⒪㈝ຓᡂ㻌 㻌 㻌
㻌 㻌 㻌 㻌 㻌 ண㜵᥋✀㻌 Ꮫᰯಖ㻌 デᴗ䠄⪁ேಖ䠅
ᗣᡭᖒ㻌 㻌 㻌
㻌 㻌 㻌 㻌 ஙᗂඣ་⒪㈝ຓᡂ㻌 㻌 㻌
㻌 㻌 㻌 㻌 ẕᏊᐙᗞ་⒪㈝ຓᡂ㻌 㻌 㻌 㻌 㻌
㻌 㻌 㻌 㻌 㔜ᗘᚰ㌟㞀ᐖ⪅་⒪㈝ຓᡂ㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌
㻌 㻌 ་⒪ಖ䠄ᅜẸᗣಖ㝤䞉♫ಖ㝤䞉ྛ✀ඹ῭䞉⯪ဨ䛺䛹䠅㻌㻌 㻌 ㏥⫋⪅་⒪㻌㻌 ⪁ேಖ་⒪㻌㻌
㻌 㻌 㻌 㻌 ᑠඣ៏ᛶ≉ᐃᝈ⒪◊✲ᴗ㻌 ≉ᐃᝈ⒪◊✲ᴗ㻌 㻌 㻌
㻌 㻌 㻌 㻌 ⮬❧ᨭ་⒪䠄⫱ᡂ་⒪䠅㻌 ⮬❧ᨭ་⒪䠄᭦⏕་⒪䠅㻌 㻌 㻌
㻌 㻌 㻌 㻌 ⮬❧ᨭ་⒪䠄⢭⚄㏻㝔་⒪䠅㻌 㻌 㻌 㻌 㻌
㻌 㻌 㻌 㻌 㧗㢠⒪㣴㈝䚸㧗㢠་⒪㈝ไᗘ㻌㻌䊻ᶆ‽㈇ᢸ㝈ᗘ㢠ㄆᐃド䠄ධ㝔䛾䜏䠅㻌㻌
ಖ
䞉
་
⒪ ಖ 㞀㻌
බ㈝㈇ᢸ
ຓᡂไᗘ㻌
⫱ᡂ་⒪䠄ඣ❺⚟♴ἲ䠅㻌
᭦⏕་⒪䠄㌟య㞀ᐖ⪅⚟♴ἲ䠅㻌㻌㻌㻌
⢭⚄㏻㝔་⒪㈝ຓᡂ㻌㻌㻌㻌㻌㻌㻌㻌㻌㻌㻌㻌㻌㻌㻌㻌㻌
⫱ᡂ་⒪䠄䠍䠔ṓᮍ‶䠅䠖㌟య䛻㞀ᐖ䛾䛒䜛ඣ❺ཪ䛿䛭䛾䜎䜎ᨺ⨨㻌 㻌 㻌 䛩䜛䛸ᑗ᮶㞀ᐖ䜢ṧ䛩䛸ㄆ䜑䜙䜜䜛ᝈ䛜䛒䜛ඣ❺
᭦⏕་⒪䠄䠍䠔ṓ௨ୖ䠅䠖㌟య㞀ᐖ⪅⚟♴ἲ➨䠐᮲䛻つᐃ䛩䜛㌟య㻌 㻌 㻌 㞀ᐖ⪅䛷䚸䛭䛾
㞀ᐖ䜢㝖ཤ䞉㍍ῶ䛩䜛ᡭ⾡➼䛾⒪㻌
㻌 㻌䛻䜘䛳䛶☜ᐇ䛻ຠᯝ䛜ᮇᚅ䛷䛝䜛䜒䛾䛻ᑐ䛧䛶ᥦ౪䛥䜜䜛䚸᭦⏕
㻌 㻌 䛾䛯䜑䛻ᚲせ䛺⮬❧ᨭ་⒪㈝䛾ᨭ⤥䜢⾜䛖䜒䛾䚹
⮬❧ᨭ་⒪䠄⫱ᡂ་⒪䠋᭦⏕་⒪䠅㻌 㻌
㌟య㞀ᐖ⪅ᡭᖒ䠄4⣭䠅㻌 䠇㻌 ᭦⏕་⒪䠄䠍䠔ṓ௨ୖ䠅
ᴾᵐᵎᵎᵔ࠰ᴾᨦܹᎍᐯᇌૅੲඥỆợụᐯᇌૅੲҔၲỆɟΨ҄ᴾ 㻌 㻌 ⫱ᡂ་⒪㻌
㻌 㻌 ᭦⏕་⒪㻌
㻌 㻌 ⢭⚄㏻㝔་⒪㈝ຓᡂ㻌
ᚰ⮚ᡭ⾡䞉䜹䝔䞊䝔䝹⒪䛾་⒪㈝ຓᡂ
ᑠඣ៏ᛶ≉ᐃᝈ⒪◊✲ᴗ䠄514ᝈ䠅 㻌 㻌 ඣ❺⚟♴ἲ䛻䜒䛸䛵䛟ᚰ⮚䛾ෆ⛉ⓗ⒪䜈䛾⿵ຓ
㻌 㻌 ྡ䛤䛸䛻ᇶ‽㻌 ⤒㐣ほᐹ䛺䛹䛿㐺⏝䛥䜜䛺䛔
≉ᐃᝈ⒪◊✲ᴗ䠄56ᝈ䠅
㻌 㻌 ᕼᑡᛶ䚸⒪ἲ䛜☜❧䛧䛶䛔䛺䛔ᝈ䛜ᑐ㇟
㻌 㻌 ⒪◊✲ᴗ䛸䛔䛖ᅜ䛾ண⟬ᴗ
㻌 㻌 ᑠඣ䛛䜙䛾⥅⥆ⓗ䛺⒪⿵ຓ䛸䛺䛳䛶䛔䛺䛔䚹
㞴࣭៏ᛶᝈᑐ⟇㸦ᑠ៏㸭≉ᐃᝈ㸧㻌 㻌
ຓ ෆ⛉ⓗ⒪䜈䛾་⒪㈝ຓᡂ
㞴ᛶᝈඞ᭹◊✲ᴗ䠄130ᝈ䠅
㻌 ᩘ䛜ᑡ䛺䛟䚸ཎᅉ᫂䛷⒪᪉ἲ䜒ᮍ☜❧䛷䛒䜚䚸䛛䛴⏕ά 㠃䛷㛗ᮇ䛻䜟䛯䜛ᨭ㞀䛜䛒䜛ᝈ䛻䛴䛔䛶䚸◊✲⌜䜢タ⨨䛧䚸ཎᅉ 䛾✲᫂䚸⒪᪉ἲ䛾☜❧䛻ྥ䛡䛯◊✲䜢⾜䛖䜒䛾䚹
㞀ᐖ⪅⥲ྜᨭἲ䠖㞀ᐖ⪅䛾ᐃ⩏䛻
㞴
䛜㏣ຍ⬨㧊ᑠ⬻ኚᛶ㻌 䝅䝱䜲䞉䝗䝺䞊䜺䞊ೃ⩌㻌 䝰䝲䝰䝲
䠄䜴䜱䝸䝇ື⬦㍯㛢ሰ䠅㻌 ṇᖖᅽỈ㢌㻌 ከⓎᛶ◳㻌 㔜➽↓ຊ㻌 䜼䝷䞁䞉䝞䝺䞊ೃ⩌㻌 䝣䜱䝑䝅䝱䞊ೃ⩌㻌
៏ᛶ⅖ᛶ⬺㧊ᛶከⓎ⚄⤒⅖㻌 ከᕢᛶ㐠ື䝙䝳䞊䝻䝟䝏䞊 䠄䝹䜲䝇䞉䝃䝮䝘䞊ೃ⩌䠅㻌 ༢䜽䝻䞊䞁ᢠయ䜢క䛖ᮎᲈ⚄⤒⅖ 䠄䜽䝻䜴䞉䝣䜹䝉ೃ⩌䠅 㻌
➽ⴎ⦰ᛶഃ⣴◳㻌
⬨㧊ᛶ➽ⴎ⦰㻌
⌫⬨㧊ᛶ➽ⴎ⦰㻌
⬨㧊✵Ὕ㻌 䝟䞊䜻䞁䝋䞁㻌 䝝䞁䝏䞁䝖䞁㻌 㐍⾜ᛶ᰾ୖᛶ㯞⑷㻌
⥺᮲య㯮㉁ኚᛶ㻌 䝨䝹䜸䜻䝅䝋䞊䝮㻌 䝷䜲䝋䝌䞊䝮㻌 䜽䝻䜲䝒䝣䜵䝹䝖䞉䝲䝁䝤㻌 䝀䝹䝇䝖䝬䞁䞉䝇䝖䝻䜲䝇䝷䞊䞉 㻌 䝅䝱䜲䞁䜹䞊䠄GSS䠅 㻌
⮴Ṛᛶᐙ᪘ᛶ╀㻌 ளᛴᛶ◳ᛶ⬻⅖(SSPE) 㻌 㐍⾜ᛶከᕢᛶⓑ㉁⬻䠄PML䠅㻌 ᚋ⦪㠌ᖏ㦵 㻌 㯤Ⰽ㠌ᖏ㦵 㻌 ๓⦪㠌ᖏ㦵㻌 ᗈ⠊⬨ᰕ⟶⊃✽㻌
≉Ⓨᛶ⭣㦵㢌ቯṚ㻌
≉Ⓨᛶ䝇䝔䝻䜲䝗ᛶ㦵ቯṚ㻌
⥙⭷Ⰽ⣲ኚᛶ㻌 ຍ㱋㯤ᩬኚᛶ㻌 㞴ᛶど⚄⤒㻌
✺Ⓨᛶ㞴⫈㻌
≉Ⓨᛶ୧ഃᛶឤ㡢㞴⫈ 㻌
࣓ࢽ࢚࣮ࣝ㻌 㐜ⓎᛶෆࣜࣥࣃỈ⭘㻌 PRLศἪ␗ᖖ㻌 ࢦࢼࢻࢺࣟࣆࣥศἪ␗ᖖ㻌 ADHศἪ␗ᖖ㻌
୰ᯡᛶᦤ㣗␗ᖖ㻌 ཎⓎᛶࣝࢻࢫࢸࣟࣥ㻌 ഇᛶపࣝࢻࢫࢸࣟࣥ㻌 ࢢࣝࢥࢥࣝࢳࢥࢻᢠ㻌
⭈㓝⣲Ḟᦆ㻌
⭈పᙧᡂ(ࢪࢯࣥ)㻌 ഇᛶ⏥≧⭢ᶵ⬟పୗ 㻌
ࣅࢱ࣑ࣥDཷᐜᶵᵓ␗ᖖ 㻌 TSHཷᐜయ␗ᖖ㻌
⏥≧⭢࣍ࣝࣔࣥᛂ 㻌
⏕Ⰻᛶ㈋⾑㻌
⁐⾑ᛶ㈋⾑㻌 㸦⮬ᕫචᛶ⁐⾑ᛶ㈋⾑䞉
Ⓨసᛶኪ㛫⾑Ⰽ⣲ᒀ㸧㻌
ᛂᛶ㈋⾑(㦵㧊␗ᙧᡂೃ⩌)㻌 㦵㧊⥺⥔㻌
≉Ⓨᛶ⾑ᰦ㻌
⾑ᰦᛶ⾑ᑠᯈῶᑡᛶ⣸ᩬ㻌
≉Ⓨᛶ⾑ᑠᯈῶᑡᛶ⣸ᩬ㻌 㹇㹥㸿⭈ 㻌 ᛴ㏿㐍⾜ᛶ⣒⌫య⭈⅖ 㻌 㞴ᛶࢿࣇ࣮ࣟࢮೃ⩌㻌 ከⓎᛶᄞ⬊⭈ 㻌
⫧ᆺᚰ➽㻌
≉Ⓨᛶᣑᙇᆺ䠄䛖䛳⾑ᆺ䠅ᚰ➽
ᣊ᮰ᆺᚰ➽㻌
࣑ࢺࢥࣥࢻࣜ
㻲㼍㼎㼞㼥
ᐙ᪘ᛶ✺↛Ṛೃ⩌
ཎⓎᛶ㧗⬡⾑
≉Ⓨᛶ㛫㉁ᛶ⫵⅖ ࢧࣝࢥࢻ࣮ࢩࢫ ࡧࡲࢇᛶỗ⣽Ẽ⟶ᨭ⅖㻌
₽⒆ᛶ⭠⅖ ࢡ࣮ࣟࣥ
⮬ᕫචᛶ⫢⅖ ཎⓎᛶ⫹Ồᛶ⫢◳ኚ
⫢⅖
≉Ⓨᛶ㛛⬦ᅽஹ㐍㻌
⫢እ㛛⬦㛢ሰ
㻮㼡㼐㼐㻙㻯㼔㼕㼍㼞㼕ೃ⩌㻌
⫢ෆ⤖▼
⫢ෆ⫹⟶㞀ᐖ
⮅ᄞ⬊⥺⥔
㔜ᛴᛶ⮅⅖
៏ᛶ⮅⅖
࣑ࣟࢻ࣮ࢩࢫ
࣮࣋ࢳ࢙ࢵࢺ
㌟ᛶ࢚ࣜࢸ࣐ࢺ࣮ࢹࢫ ከⓎᛶ➽⅖࣭⓶➽⅖ ࢩ࢙࣮ࢢࣞࣥೃ⩌
ᡂேࢫࢸࣝ
㧗Ᏻ䠄ື⬦⅖ೃ⩌䠅㻌
ࣂ࣮ࢪ࣮ࣕ
⤖⠇ᛶከⓎື⬦⅖
࢙࢘ࢤࢼ࣮⫗ⱆ⭘
ࣞࣝࢠ࣮ᛶ⫗ⱆ⭘ᛶ⾑⟶⅖
ᝏᛶ㛵⠇࣐ࣜ࢘ࢳ
ഃ㢌ື⬦⅖ ᢠࣜࣥ⬡㉁ᢠయೃ⩌
ᙉ⓶
ዲ㓟⌫ᛶ➽⭷⅖
◳ᛶⴎ⦰ᛶⱏⓄ
ཎⓎᛶචೃ⩌
ⱝᖺᛶ⫵Ẽ⭘
ࣛࣥࢤࣝࣁࣥࢫ⣽⬊⤌⧊⌫
⫧‶పẼೃ⩌
⫵⬊పẼೃ⩌㻌
⫵ື⬦ᛶ⫵㧗⾑ᅽ
៏ᛶ⾑ᰦሰᰦᛶ⫵㧗⾑ᅽ
ΰྜᛶ⤖ྜ⤌⧊
⚄⤒⥺⥔⭘䊠ᆺ㻌 㸦ࣞࢵࢡࣜࣥࢢࣁ࢘ࢮࣥ㸧㻌
⚄⤒⥺⥔⭘䊡ᆺ
⤖⠇ᛶ◳㻔ࣉࣜࣥࢢࣝ㻕
⾲⓶Ỉ⑁
⮋⑁ᛶⓄ㻌 ኳ⑁⒔㻌
⬻⓶㉁ᇶᗏ᰾ኚᛶ
㔜ከᙧⁱฟᛶ⣚ᩬ㻔ᛴᛶᮇ㻕
ࣜࣥࣃ⬦⟶➽⭘㻔㹊㸿㹋㻕 㐍⾜ᛶ㦵ᛶ⥺⥔␗ᙧᡂ㻔㻲㻻㻼㻕 Ⰽ⣲ᛶ⓶㻔㼄㻼㻕 ࢫࣔࣥ
ୗᆶయᶵ⬟పୗ
ࢡࢵࢩࣥࢢ
ඛ➃ᕧ
ཎⓎᛶഃ⣴◳
᭷Ჲ㉥⾑⌫ࢆక࠺⯙㋃
㹆㹒㹊㹔㸫㸯㛵㐃⬨㧊㻔㹆㸿㹋㻕 ඛኳᛶ㨶㫣Ⓞᵝ⣚⓶
ඛኳᛶᚰᝈ
㻌 䝏䜰䝜䞊䝊䛾䛒䜛ᝈ 㻌 㻌 㻌 䠄SpO2<85%? , 90%?䠅 㻌 䝣䜷䞁䝍䞁ᆺᚠ⎔
㻌 㻌 㻌 䠄༢ᚰᐊ䚸୕ᑤᘚ㛢㙐䚸䞉䞉䞉䠅 㻌 ྑᚰᐊ䜢యᚰᐊ䛸䛩䜛ᝈ 㻌 㻌 㻌 䠄ಟṇ⾑⟶㌿䚸䞉䞉䞉䠅 㻌 ᘚ㏫ὶ䛜ၥ㢟䛸䛺䜛ᝈ 㻌 㻌 㻌 䠄䝣䜯䝻䞊ᅄᚩ⾡ᚋ䚸䞉䞉䞉䠅
䛺䛹
ຓᡂᑐ㇟⪅
㻌 㻌 ㌟య㞀ᐖ⪅ᡭᖒ䠍⣭䞉䠎⣭
㻌 㻌 㻌 㻌
㻌 㻌 ⒪⫱ᡭᖒ䠝⣭
㔜ᗘᚰ㌟㞀ᐖ⪅་⒪㈝ຓᡂไᗘ㻌 㻌
ຓᡂᑐ㇟⪅
㻌 㻌 ㌟య㞀ᐖ⪅ᡭᖒ䠍⣭䞉䠎⣭
㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 䠄ᆅᇦ䛻䜘䛳䛶䛿䠍䡚䠏⣭䠖20㒔┴䠅 㻌 㻌 ⒪⫱ᡭᖒ䠝⣭
㻌 㻌 ⒪⫱ᡭᖒ䠞⣭䠄୰ᗘ䠅䛸㌟య㞀ᐖ⪅ᡭᖒ䠄䠏⣭䡚䠒⣭䠅
⏕ά䜢ᨭ䛘䜛♫ಖ㞀ไᗘ䠄♫ᢇຓ䠅㻌
ᖺ㱋㻌㻌 㻌 㻌 ㄌ⏕䠄䠌ṓ䠅㻌㻌ᑵᏛ๓㻌㻌 ᑵᏛᮇ㻌 䠄䠒ṓ䡚㻝㻤ṓ䠅㻌㻌
Ꮚ⫱䛶䞉ᑵປᮇ㻌
䠄㻞㻜ṓ䡚㻌 㻠㻜ṓ㻌 ㏥⫋ᚋ㻌 䠄㻢㻡ṓ䡚㻌 㻣㻜ṓ䡚㻌㻌
㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌
ฟ⏘⫱ඣ୍㔠㻌㻌 㻌 㻌
ඣ❺ᡭᙜ㻌
Ꮚ䛹䜒䛾䛯䜑䛾ᡭᙜ㻌㻌㻥ṓ㻌 ඣ❺ᢇ㣴ᡭᙜ㻌㻌㻌㻌㻌㻌㻌㻌㻌㻌㻌㻌㻌㻌㻌㻝㻤ṓ㻌㻌
≉ูඣ❺ᢇ㣴ᡭᙜ㻌
㻌
㞀
㞀ᐖඣ⚟♴ᡭᙜ㻌㻌 㻞㻜ṓ䡚≉ู㞀ᐖ⪅ᡭᙜ㻌
㑇᪘ᖺ㔠㻌㻌 㻌 㻌 㻌 㻌 㻌㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌
㞀ᐖᖺ㔠㻌
㻌 㻌 㻌 䠄㞀ᐖᇶ♏ᖺ㔠䚸㞀ᐖཌ⏕ᖺ㔠䠅㻌
㻌 㻌
⪁㱋ᖺ㔠㻌㻌㻌 㻌 㻌 㻌
⏕άಖㆤ㻌㻌㻌 㻌 㻌 㻌 㻌 㻌㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻝㻤ṓ㻌㻌ປ⅏䞉㞠⏝ಖ㝤㻌
㻌㻌㻌㻌㻌䠄㞀ᐖᖺ㔠䚸യᡭᙜ㔠䠅㻌 㻌 㻌 ⏕ά⚟♴㈨㔠㈚ไᗘ㻌 㻌 㻌㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 ⊂❧⾜ᨻἲேᨾᑐ⟇ᶵᵓ䛻䜘䜛ㆤᩱ➼⿵ൾ㻌 㻌 㻌 㻌 㻌
ᡤ ᚓ ಖ 㞀 ไ ᗘ㻌
ᖺ㔠ไᗘ
ᅜẸᖺ㔠䛻ຍධ䛧䛶䛔䜛㛫䛻ึデ᪥䠄㞀ᐖ䛾ཎᅉ䛸䛺䛳䛯Ẽ䜔䜿䜺 䛻䛴䛔䛶䚸ึ䜑䛶་ᖌ䛾デ⒪䜢ཷ䛡䛯᪥䠅䛾䛒䜛Ẽ䜔䜿䜺䛷䚸ἲ௧ 䛻䜘䜚ᐃ䜑䜙䜜䛯㞀ᐖ➼⣭䠄䠍⣭䞉䠎⣭䠅䛻䜘䜛㞀ᐖ䛾≧ែ䛻䛒䜛㛫䛿 㞀ᐖᇶ♏ᖺ㔠䛜ᨭ⤥䛥䜜䜛䚹
ᨭ⤥㢠䠄ᐃ㢠䠅㻌 1⣭ 966,000 䠄᭶㢠㻌 80,500䠅 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 㻌 2⣭ 772,800 䠄᭶㢠㻌 64,400䠅
ͤ 䠍䠔ṓ฿㐩ᖺᗘ䛾ᮎ᪥䜎䛷䛻䛒䜛Ꮚ䠄㞀ᐖ⪅䛿䠎䠌ṓᮍ‶䠅䛜䛔䜛ሙྜ䛿䚸 㻌 㻌 Ꮚ䛾ேᩘ䛻䜘䛳䛶ຍ⟬䛜⾜䜟䜜䜎䛩䚹
ͤ 㞀ᐖᇶ♏ᖺ㔠䜢ཷ䛡䜛䛯䜑䛻䛿䚸ึデ᪥䛾䛒䜛᭶䛾๓䚻᭶䜎䛷䛾බⓗᖺ㔠䛾㻌 㻌 㻌 ຍධᮇ㛫䛾䠎䠋䠏௨ୖ䛾ᮇ㛫䛻䛴䛔䛶䚸ಖ㝤ᩱ䛜⣡ཪ䛿ච㝖䛥䜜䛶䛔䜛䛣䛸䚸 㻌 㻌 䜎䛯䛿ึデ᪥䛾䛒䜛᭶䛾๓䚻᭶䜎䛷䛾䠍ᖺ㛫䛻ಖ㝤ᩱ䛾ᮍ⣡䛜䛺䛔䛣䛸 㻌 㻌 䠄ಖ㝤ᩱ⣡せ௳䠅䛜ᚲせ䚹
㞀ᐖᇶ♏ᖺ㔠㻌 㻌
ͤ㻌 ཌ⏕ᖺ㔠ຍධ୰䛻ึデ᪥䛜䛒䜜䜀䚸㞀ᐖཌ⏕ᖺ㔠䛻䛺䜚䜎䛩䚹
┿㠃┠䛻䜢䛧䛶䛔䛶䜒䚸ඛኳᛶᚰᝈᝈ⪅䛿䚸 㞀ᐖཌ⏕ᖺ㔠䛾ᑐ㇟䛻䛿䛺䜙䛺䛔䚹
Department of Pediatric Cardiology, Children‘s Medical Center, Ehime University Hospital 䛆1⣭䛇䠄ሗ㓘ẚ䛾ᖺ㔠㢠䠅 㽢 1.25 + 䛊㓄അ⪅䛾ຍ⤥ᖺ㔠㢠䠄222,400䠅䛋 䛆2⣭䛇䠄ሗ㓘ẚ䛾ᖺ㔠㢠䠅 + 䛊㓄അ⪅䛾ຍ⤥ᖺ㔠㢠䠄222,400䠅䛋ͤ
䛆3⣭䛇䠄ሗ㓘ẚ䛾ᖺ㔠㢠䠅 ͤ᭱పಖ㞀㢠㻌579,700㻌 㻌 㻌ͤᑐ㇟⪅䛾䜏
ึデ᪥䛜ຍධᮇ㛫୰䛷䛺䛔䟿
㞀ᐖཌ⏕ᖺ㔠㻌 㻌
ཌ⏕ᖺ㔠䛻ຍධ䛧䛶䛔䜛㛫䛻ึデ᪥䛾䛒䜛Ẽ䜔䜿䜺䛷 㞀ᐖᇶ♏ᖺ㔠䛾1⣭䜎䛯䛿2⣭䛻ヱᙜ䛩䜛㞀ᐖ䛾≧ែ䛻 䛺䛳䛯䛸䛝䛿䚸㞀ᐖᇶ♏ᖺ㔠䛻ୖ䛫䛧䛶㞀ᐖཌ⏕ᖺ㔠䛜 ᨭ⤥䛥䜜䜛䚹
䜎䛯䚸㞀ᐖ䛾≧ែ䛜2⣭䛻ヱᙜ䛧䛺䛔㍍䛔⛬ᗘ䛾㞀ᐖ䛾䛸 䛝䛿3⣭䛾㞀ᐖཌ⏕ᖺ㔠䛜ᨭ⤥䛥䜜䜛䚹
≉ูඣ❺ᢇ㣴㻌㻌 ᡭᙜ㻌
䠍⣭᭶㢠㻌 㻡㻜㻘㻠㻜㻜㻌 䠍⣭᭶㢠㻌 㻡㻜㻘㻜㻡㻜㻌 䠎⣭᭶㢠㻌 㻟㻟㻘㻡㻣㻜㻌 䠎⣭᭶㢠㻌 㻟㻟㻘㻟㻟㻜㻌 㞀ᐖඣ⚟♴㻌
ᡭᙜ㻌 㻝㻠㻘㻞㻤㻜㻌 㻌 㻝㻠㻘㻝㻤㻜㻌 㻌
≉ู㞀ᐖ⪅㻌
ᡭᙜ㻌 㻞㻢㻘㻞㻢㻜㻌 㻞㻢㻘㻜㻤㻜㻌
㞀ᐖᇶ♏ᖺ㔠㻌
䠍⣭᭶㢠㻌 㻤㻝㻘㻥㻞㻡㻌 㻌䠍⣭᭶㢠㻌 㻤㻜㻘㻡㻜㻜㻌㻌 㻌 㻌 ᖺ㢠㻌 㻥㻤㻟㻘㻝㻜㻜㻌 㻌 㻌 ᖺ㢠㻌㻥㻢㻢㻘㻜㻜㻜㻌 䠎⣭᭶㢠㻌 㻢㻡㻘㻡㻠㻝㻌 䠎⣭᭶㢠㻌 㻢㻠㻘㻠㻜㻜㻌 㻌 㻌 ᖺ㢠㻌 㻣㻤㻢㻘㻡㻜㻜㻌 㻌 㻌 ᖺ㢠㻌㻣㻣㻞㻘㻤㻜㻜㻌 㻞㻜㻝㻟ᖺ㻝㻜᭶䛛䜙ᖺ㔠㻝㻚㻜䠂䚸ᡭᙜ㻜㻚㻣䠂䛾ᘬ䛝ୗ䛢㻌
ᡭᙜ䞉㞀ᐖᖺ㔠㢠
㻞㻜㻝㻟ᖺ㻝㻜᭶䡚
ᖺ㔠㻞㻚㻡䠂䚸ᡭᙜ㻝㻚㻣䠂䛾ẁ㝵ⓗᘬ䛝ୗ䛢㻌
㻞㻜ṓ๓യ䛻䜘䜛㞀ᐖᇶ♏ᖺ㔠䛻䛛䛛䜛ᡤᚓไ㝈㻌
㻌20ṓ๓䛻യ䜢㈇䛳䛯ே䛾㞀ᐖᇶ♏ᖺ㔠䛻䛴䛔䛶䛿䚸ᮏே䛜ಖ
㝤ᩱ䜢⣡䛧䛶䛔䛺䛔䛣䛸䛛䜙䚸ᡤᚓไ㝈䛜タ䛡䜙䜜䛶䛔䜛䚹 㻌 ᡤᚓ㢠䛜3604ᖸ䠄ᢇ㣴ᐙ᪘䛺䛧䠅䜢㉸䛘䜛ሙྜ䛻䛿ᖺ㔠㢠䛾 2ศ䛾1┦ᙜ㢠䛻㝈䜚ᨭ⤥Ṇ䛸䛧䚸4621ᖸ䜢㉸䛘䜛ሙྜ䛻䛿
㢠ᨭ⤥Ṇ䛸䛩䜛ẁ㝵ไ䛜䛸䜙䜜䛶䛔䜛䚹
ᢇ㣴ᐙ᪘ 0ே 1ே 2ே 3ே 䠇1ே䛷ቑ㢠
ℐ悐㓗䴎 㬊 4,621,000 5,001,000 5,381,000 5,761,000 380,000 烀/烁㓗䴎 㬊 3,604,000 3,984,000 4,364,000 4,744,000 380,000
䠍㻛䠎㻌 ᨭ⤥Ṇ㻌
㻌 㻌0㻌 㻌 㻌 㻌 㻌 360.4㻌 㻌 㻌 462.1㻌 㻌 䠄ᡤᚓ䠅
㢠ᨭ⤥㻌
㢠㻌 ᨭ⤥Ṇ㻌
୍⯡㞠⏝䛻ྥ䛡䛯ᨭ⟇㻌
⚟♴⟇䛻䜘䜛ᑵປᨭ㻌 㻌 㻌
㞀ᐖ⪅⫋ᴗ⬟ຊ㛤Ⓨᰯ
➼䛻䜘䜛බඹ⫋ᴗカ⦎
බඹ⫋ᴗᏳᐃᡤ䠄䝝䝻䞊䝽䞊䜽䠅 ᆅᇦ㞀ᐖ⪅⫋ᴗ䝉䞁䝍䞊 㞀ᐖ⪅ᑵᴗ䞉⏕άᨭ䝉䞁䝍䞊
ᑵປ⛣⾜ᨭ
ᑵປ⥅⥆ᨭ
䠞ᆺ
ᑵປ⥅⥆ᨭ
⏕άㆤ 䠝ᆺ
ᆅᇦάືᨭ䝉䞁䝍䞊
⮬❧カ⦎
䠄⏕άカ⦎䠅 ᅾᏯᑵᴗ
୍⯡㞠⏝
୍⯡㞠⏝䛺䛹
㞠⏝⟇
⚟♴⟇
㐃ᦠ
ᑵປᨭ⟇䛾య⣔㻌㻌 㻌
ᑵປ㛵㐃⟇䛾యീ
㞀ᐖ⪅⥲ྜᨭἲ 㞀ᐖ⪅㞠⏝ಁ㐍ἲ
䠄ᖹᡂ25ᖺ4᭶1᪥䡚䠅
㞠⏝㛵ಀ䛜䛒䜛
㞠⏝ಖ㝤䛻ຍධ䛩䜛
ᮏẼ䛾䛜䛷䛝䜛
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9:00䡚18:00䛾䛖䛱䚸4㛫ົ䡚䚸యㄪ䛻ྜ䜟䛫䛶
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䝟䝋䝁䞁ᴗົ䚸⎔ቃᴗ䚸䝔䞊䝥㉳䛣䛧䚸ฟᙇ䜹䝣䜵
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㞀ᐖ⪅ᑵປ⥅⥆ᨭᴗ䠄䠝ᆺ䠅㻌㻌 㻌
ᙇ䜹䝣䜵
Department of Pediatric Cardiology, Children‘s Medical Center, Ehime University Hospital