㸦ㄽᩥ༤ኈ㸧㸦ᵝᘧ 㸦ㄽᩥ༤ኈ㸧㸦ᵝᘧ 㸦ㄽᩥ༤ኈ㸧㸦ᵝᘧ 㸦ㄽᩥ༤ኈ㸧㸦ᵝᘧ 7㸧㸧㸧㸧
ᶫᮏ ⱥ᫂ ẶࡽᏛ⏦ㄳࡢࡓࡵᥦฟࡉࢀࡓㄽᩥࡢᑂᰝせ᪨
㢟 ┠
ㄽᩥ㸸
Ultra-Wide-Field Fundus Autofluorescence in Multiple Evanescent White Dot Syndrome
㸦 ከⓎᾘኻᛶⓑⅬೃ⩌ࡢ㉸ᗈゅ⮬Ⓨ⺯ගീ 㸧
American Journal of Ophthalmology 159:698-706, 2015 Hideaki Hashimoto, Shoji Kishi
ㄽᩥ㸸
Shortening of the rod outer segment in Oguchi disease 㸦 ᑠཱྀẶ࠾ࡅࡿᱰయ⣽⬊እ⠇ࡢ▷⦰ 㸧
Graefe’s Archive Clinical Experimental Ophthalmology 247:1561-1563, 2009 Hideaki Hashimoto, Shoji Kishi
ㄽᩥࡢせ᪨ཬࡧุᐃ⌮⏤
ㄽᩥ
ከⓎᾘኻᛶⓑⅬೃ⩌0(:'6ࠊ࣑࣮ࣗࢬࡣࠊ㏆どࡢⱝᖺ⪅ዲⓎࡋࠊ∦║
ࡢᛴ⃭࡞どຊపୗࢆࡁࡓࡍࠋⓎࡣ⮬ᕫචࡢ㛵ࡀ᥎ᐃࡉࢀ࡚࠸ࡿࠋ᳨║
㙾ⓗࡣ║ᗏῐ࠸ⓑᩬࡀከᩘฟ⌧ࡍࡿࡀࠊ㐌㛫⛬ᗘ࡛ᾘኻࡍࡿࠋどຊపୗࡶ
᭶⛬ᗘ࡛⮬↛ᅇࡍࡿࠋගᖸ΅᩿ᒙィ࡛ࡣࠊ⥙⭷ど⣽⬊እ⠇ࡢࡧ៏ᛶࡢ◚
ቯࡀほᐹࡉࢀࡿࡀࠊⓑᩬࡣᚲࡎࡋࡶ୍⮴ࡋ࡞࠸ࠋ0(:'6㸦࣑࣮ࣗࢬ㸧ࡣ᳨║㙾 ᡤぢࡀஈࡋ࠸ࡓࡵࠊᕢࡀࡇࡽⓎࡋࠊࡢࡼ࠺ᗈࡀࡾࠊࡢࡼ࠺ᾘ
㏥ࡍࡿࡢࡣ࡛᫂࠶ࡗࡓࠋⴭ⪅ࡽࡣ㉸ᗈゅ⮬Ⓨ⺯ගᙳ⨨㸦࢜ࣉࢺࢫ㸧ࢆ
⏝࠸࡚ࠊ0(:'6ࡢែࢆほᐹࡋࡓࠋᑐ㇟ࡣ0(:'6ᝈ⪅║࡛ࠊᖺ㱋ࡣ㹼 ṓࠋ⤒㐣ほᐹᮇ㛫ࡣࠊ㹼᭶࡛࠶ࡗࡓࠋᝈ║ࡢึデ▹ṇどຊࡣࠊ㹼ࠋ ᒅᢡࡣᖹᆒ'㸦ࢪ࢜ࣉࢱ࣮㸧ࡢ㏆ど࡛࠶ࡗࡓࠋ0(:'6ࡢᛴᛶᮇࡽᐶゎᮇ
ࡅ࡚ࠊ࢜ࣉࢺࢫ࡛⮬Ⓨ⺯ගࡀஹ㐍ࡋࡓ㡿ᇦࡢほᐹࠊගᖸ΅᩿ᒙィ࡛⥙⭷ࡢ
⌮ᡤぢࡢホ౯ࢆ⾜ࡗࡓࠋ0(:'6ࡢึᮇኚࡣࠊど⚄⤒ங㢌㯤ᩬࢆྵࡴ║ᗏᚋᴟ 㒊ࡽࡧ៏ᛶጞࡲࡾࠊ࿘ᅖᩬ≧ࡢ㐣⺯ගࢆక࠸ࠊࡇࢀࡣ║ᗏࡢῐ࠸ⓑᩬ
୍⮴ࡋ࡚࠸ࡓࠋගᖸ΅᩿ᒙィ࡛ࡣど⣽⬊ࡢࡧ៏ᛶࡢ◚ቯ┦ᙜࡋࡓࠋ㐣⺯ග
ᕢࡣᛴᛶᮇ࡛ࡣ࿘㎶㐲ᚰᛶᣑࡋࠊࡑࡢᚋࠊ࿘㎶ࡽᾘ㏥ࡀጞࡲࡾࠊᐶゎ ᮇ࡛ࡣᚋᴟ㒊㐣⺯ගᕢࡀ᮰ࡋࠊᚎࠎ㐣⺯ගࢆኻࡗ࡚࠸ࡗࡓࠋ⮬Ⓨ⺯ග ࡣ◚ቯࡉࢀࡓど⣽⬊እ⠇ࠊࡑࢀࢆ㈎㣗ࡋࡓ࣐ࢡࣟࣇ࣮ࢪࠊࡑࡋ࡚㞀ᐖࢆཷࡅ ࡓ⥙⭷Ⰽ⣲ୖ⓶ࡀࡑࡢࢯ࣮ࢫ࡞ࡿࠋⴭ⪅ࡽࡣࠊᮏࢆᘬࡁ㉳ࡇࡍ㧊ᾮ୰ࡢ⮬
ᕫᢠయࡀど⚄⤒ங㢌ࡢ⦕ࡽ⥙⭷ୗධࡋࠊ║ᗏ࿘㎶ᗈࡀࡿࡢ࡛ࡣ࡞࠸
᥎ㄽࡋࡓࠋ0(:'6࡛ࡣ║ᗏࡀṇᖖ࡞║ࡶど㔝␗ᖖࡀࡋࡤࡋࡤⓎࡍࡿࠋ㧊 ᾮ୰ࡢᢠయࡀ║ࡢど⚄⤒ࡶ㞀ᐖࡍࡿ⪃࠼ࢀࡤㄝ᫂ࡀྍ⬟࡛࠶ࡿࠋ
ᮏ◊✲ࡼࡾࠊᚑ᮶࡛᫂࠶ࡗࡓ0(:'6ࡢᕢࡢ㐍⾜ᾘ㏥㐣⛬ࡀ᫂ࡽ࡞ࡗ ࡓࠋࡇࢀࡣᮏࡢⓎᶵᗎࢆ⪃࠼ࡿୖ࡛ࠊ㔜せ࡞᪂▱ぢࢆᥦ౪ࡍࡿࡶࡢ࡛࠶ࡾࠊ ༤ኈ㸦་Ꮫ㸧ࡢᏛ್ࡍࡿࡶࡢุᐃࡋࡓࠋ
㸦ᖹᡂ27ᖺ8᭶6᪥㸧 ᑂᰝጤဨ
ᰝ ⩌㤿Ꮫᩍᤵ㸦་Ꮫ⣔◊✲⛉㸧
⬻⚄⤒⏕་Ꮫศ㔝ᢸ௵ ᖹ ᏹ ༳
ᰝ ⩌㤿Ꮫᩍᤵ㸦་Ꮫ⣔◊✲⛉㸧 ⬻⚄⤒እ⛉Ꮫศ㔝ᢸ௵ ዲ ᮏ ⿱ ᖹ ༳ ᰝ ⩌㤿Ꮫᩍᤵ㸦་Ꮫ⣔◊✲⛉㸧 ⬻⚄⤒ෆ⛉Ꮫศ㔝ᢸ௵ ụ ⏣ ె ⏕ ༳