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60

61

䛔䚹䛭䜜䛻ຍ䛘䠈

trans䉄 ring

ഃ䛷䛿

ATP

䛾Ꮡᅾୗ䛷

GroES

䛾⤖ྜ䛜㉳䛣䜛䛜䠈୍ᗘ⤖ྜ

䛩䜛䛸䛭䜜௨㝆ゎ㞳䛫䛪䠈ඛ䛻ᇶ㉁䛜⤖ྜ䛧䛶䛔䛶䜒ᇶ㉁䛸ධ䜜௦䜟䜛䜘䛖䛻䛧䛶

GroES

⤖ྜ䛩䜛䚹GroEL G192Xኚ␗య䛿

cis

trans

䛹䛱䜙䛾䝸䞁䜾䛻䛚䛔䛶䜒

GroES

䛿⤖ྜ䛷䛝 䜛䛜䠈䜻䝱䝡䝔䜱ෆ㒊䛻ᇶ㉁䛜ⴠ䛸䛧㎸䜎䜜䛺䛔䚹䛧䛛䛧䠈Gly192 ṧᇶ䜢⨨᥮䛧䛯䜰䝭䝜㓟䛻䜘 䜚ᇶ㉁䛾䝸䝣䜷䞊䝹䝕䜱䞁䜾άᛶ䛻㐪䛔䛜䜏䜙䜜䛯䚹69kDa 䛾኱⭠⳦⏤᮶䛾䝬䝹䝖䝕䜻䝇䝖䝸 䞁䜾䝹䝁䝅䝎䞊䝊(MalZ)䛿䠈GroEL䛾䜻䝱䝡䝔䜱ෆ㒊䛻ໟᣓ໬䛥䜜䛪䠈

cis

䉄ringഃ䛻

GroES

䛜䠈

trans

ring

ഃ䛻

MalZ

䛜⤖ྜ䛧䛯≧ែ䛷䛾䝸䝣䜷䞊䝹䝕䜱䞁䜾䝰䝕䝹䛜ሗ࿌䛥䜜䛶䛔䜛

(93)䚹GroEL G192X

ኚ␗య䛾

cis

䉄ring 䛻䛿

ATP

㠀Ꮡᅾୗ䛷

GroES

䛜⤖ྜ䛩䜛䛾䛷

MalZ

䛾䜘䛖䛻

trans

䉄ring 䛻䛚䛔䛶

GroES

䛜⵹䜢䛧䛺䛔≧ែ䛷䛾䝸䝣䜷䞊䝹䝕䜱䞁䜾ᶵᵓ䜒

⪃䛘䜙䜜䜛䚹GroEL G192X ኚ␗య䛾䝅䝱䝨䝻䝙䞁ᶵ⬟䛾Ⓨ⌧䛻䛿

GroES

䛸䛾┦஫స⏝䛜

኱䛝䛟㛵୚䛧䛶䛔䜛䛣䛸䛜⪃䛘䜙䜜䛯䛾䛷

QCM

ἲ䜢฼⏝䛧䛯ゎᯒ䜢⾜䛳䛯䚹㻌

GroEL G192X

ኚ␗య䛿䠈ATP 䛾㠀Ꮡᅾୗ䛷䜒

GroES

䛜⤖ྜ䛧䛶䛔䜛䛾䛜ぢ䜙䜜䛯

(ᅗ 2-11)䚹䛥䜙䛻䛣䛾⤖ྜ㔞䛿⨨᥮䛧䛯䜰䝭䝜㓟ṧᇶ䛜኱䛝䛔䜋䛹䜘䜚⤖ྜ䛧䛶䛔䜛䛾䛜᫂䜙䛛䛸䛺

䛳䛯䚹䛴䜎䜚䠈G192Xኚ␗య䛿ண䜑

Open

≧ែ䛻䛺䛳䛶䛔䜛

cis䉄 ring

ഃ䛻䛚䛔䛶

ATP

䛾㠀 Ꮡᅾୗ䛷

GroES

䛸┦஫స⏝䛩䜛䛣䛸䛜䛷䛝䠈Gly192 䜢䜘䜚኱䛝䛔䜰䝭䝜㓟ṧᇶ䛻⨨᥮䛧䛯ኚ

␗య䜋䛹

GroES

䛸┦஫స⏝䛧᫆䛔䛣䛸䛜☜ㄆ䛥䜜䛯䚹ᅗ

2-12

䛻䛚䛔䛶

GroEL WT

ཬ䜃

GroEL G192N

ኚ␗య䛾

ATP

Ꮡᅾୗ䠈㠀Ꮡᅾୗ䛻䛚䛡䜛

GroES

䛸䛾┦஫స⏝ゎᯒ⤖ᯝ 䜢♧䛧䛯䚹䛣䛾⤖ᯝ䛻䛚䛔䛶䠈GroEL WT䛿

ATP

㠀Ꮡᅾୗ䜘䜚䜒Ꮡᅾୗ䛾᪉䛜

GroES

䛸⤖

ྜ䛧䛶䛔䛯䚹䛣䜜䛿䠈GroEL WT 䛻

ATP

䛜⤖ྜ䛩䜛䛸

Closed

≧ែ䛛䜙

Open

≧ែ䛻䛺䜚

GroES

䛜⤖ྜ䛷䛝䜛䜘䛖䛻䛺䜛ᛶ㉁䛜཯ᫎ䛥䜜䛶䛔䜛䛸⪃䛘䜙䜜䜛䚹GroEL G192Nኚ␗య䜒 㢮ఝ䛧䛯⤖ᯝ䜢♧䛧䛯䛣䛸䛛䜙䠈G192X ኚ␗య䛾

trans䉄 ring

䛻䛚䛡䜛䜰䝢䜹䝹䝗䝯䜲䞁䛿

ATP

㠀Ꮡᅾୗ䛷䛿

Closed

≧ែ䛷䛒䜛䛜䠈ATP䛜⤖ྜ䛩䜛䛣䛸䛷

Open

≧ែ䛸䛺䜚

GroES

䛜⤖ྜ䛧䛯䛸᥎ 䛥䜜䜛䚹䛭䛾ᚋ䠈GroEL WT䛿

ATP

䛜ຍỈศゎ䛥䜜

ADP

䛻䛺䜛䛸

GroES

䛜እ䜜䜛䚹䛧䛛䛧䠈G192X ኚ␗య䛿෌ᗘ

Closed

≧ែ䛻ᡠ䜛㝿䛻ᵓ㐀 ኚ ໬䛾ᨭⅬ䛸䛺䜛

62

Hinge䊡㒊఩䛻䛚䛡䜛 Gly192

ṧᇶ䛾䜰䝭䝜㓟ṧᇶ䛜ኚ໬䛧䛯䛣䛸䛻䜘䜚ఱ䜙䛛䛾❧య㞀ᐖ䛜

⏕䛨䜛䛣䛸䛷

Closed

≧ែ䛻ᡠ䜜䛪䠈GroES 䜒ゎ㞳䛧䛺䛟䛺䜛䛸⪃䛘䜙䜜䜛䚹GroEL 䜈䛾ኚ␗

䜢ᑟධ䛩䜛䛣䛸䛷䠈ᮏ㉁ⓗ䛺ᵓ㐀䛜ኚ໬䛩䜛䛸䠈䝅䝱䝨䝻䝙䞁ᶵ⬟䛜኱䛝䛟ኚ䜟䜛䛣䛸䛻⧅䛜䜛 䛣䛸䛜⪃䛘䜙䜜䜛䚹䜎䛯䠈ATP 䛾ຍỈศゎ䛻䜘䜚

cis

䉄ring 䛾ᵓ㐀䛿ኚ໬䛧䛺䛔䛜䠈䝸䞁䜾㛫䛾 ᥋ゐ䛻䜘䜚

trans

䉄ring 䛷䛾䝗䝯䜲䞁䛾ືస䛜⏕䛨䜛䛣䛸䛜䜽䝷䜲䜸㟁Ꮚ㢧ᚤ㙾䛻䜘䜚ゎᯒ䛥䜜 䛶䛚䜚䠈䛭䛾ᚋ

trans

䉄ring 䛾ື䛝䛻䜘䜚඲య䛾䝸䞁䜾䛜ᒎ㛤䛧䠈ATP䛸ᇶ㉁䝍䞁䝟䜽㉁䛜⤖ྜ

䛷䛝䜛䜘䛖䛻䛺䜛䛸♧䛥䜜䛶䛔䜛

(16)

Open

≧ែ䛷䛒䜛

cis

䉄ring༢⊂䛷䛾

GroEL G192X

ኚ␗య䛾䝅䝱䝨䝻䝙䞁ᶵ⬟䜢䜘䜚ヲ⣽

䛻ゎᯒ䛩䜛䛣䛸䜢┠ⓗ䛸䛧䠈GroEL䛾䝅䞁䜾䝹䝸䞁䜾ኚ␗య

SR-1 (89)䛻䛚䛡䜛 Gly192

ṧᇶ 䜢௚䛾䜰䝭䝜㓟ṧᇶ䛻⨨᥮䛧䛯ኚ␗య䜢⏝䛔䛯 ᐃ䜢⾜䛳䛯䠄ᅗ

2-13䠅䚹SR-1 G192X

ኚ␗

య䛾

ATP

ຍỈศゎ⬟ຊ䛿

GroEL WT

䛾༙ศ⛬ᗘ䛧䛛䛺䛔

SR-1 WT

䜘䜚䜒䛥䜙䛻ప䛛䛳 䛯䚹䛧䛛䛧䠈GroES䛾ῧຍ䛷䜘䜚άᛶ䛜పୗ䛧䛶䛔䛯䛣䛸䛛䜙䠈GroES䛸䛾ぶ࿴ᛶ䛜䛒䜛䛣䛸䛜

♧䛥䜜䛯䚹Rhodanese 䛾䝸䝣䜷䞊䝹䝕䜱䞁䜾άᛶ䛿

SR-1 WT

䜘䜚䜒ప䛔䛜

Spontaneous

䜘 䜚䜒㧗䛔䛣䛸䛛䜙䜻䝱䝡䝔䜱ෆ㒊䜈ᇶ㉁䜢ྲྀ䜚㎸䜣䛷䛔䜛䛣䛸䛜⪃䛘䜙䜜䜛䚹䜎䛯䠈䝅䞁䜾䝹䝸䞁䜾 ኚ␗య䛿㏻ᖖ䝅䝱䝨䝻䝙䞁䝃䜲䜽䝹䛜୍ᗘ䛧䛛ᅇ䜙䛺䛔䛂䝅䞁䜾䝹䝍䞊䞁䜸䞊䝞䞊≧ែ䛃䛷䛒 䜛䛣䛸䛛䜙䠈䜻䝱䝡䝔䜱ෆ㒊䛻ⴠ䛸䛧㎸䜎䜜䛯ኚᛶ

MDH

䛿እ䛻ᨺฟ䛥䜜䛺䛟䛺䜛䛾䛷

SR-1

␗య䛿

MDH

䛾䝸䝣䜷䞊䝹䝕䜱䞁䜾௓ຓ䜢⾜䜟䛺䛔䛸䛥䜜䛶䛔䜛(94)䚹䛧䛛䛧䠈SR-1 G192Xኚ

␗య䛾άᛶ䛿䝎䝤䝹䝸䞁䜾䛾

G192X

ኚ␗య䛾ሙྜ䛸䛿␗䛺䜚㧗䛔άᛶ䜢♧䛧䛶䛔䛯䚹䛣䜜䜘 䜚䠈SR-1 G192X ኚ␗య䛿

ATP

䛾Ꮡᅾୗ䛻䛚䛔䛶䝅䞁䜾䝹䝍䞊䞁䜸䞊䝞䞊䛷䝃䜲䜽䝹䛜೵

Ṇ䛫䛪䠈GroES䛜እ䜜䜛䛣䛸䛷

MDH

䛜እഃ䛻ᨺฟ䛥䜜䛶䛔䜛䛣䛸䜒⪃䛘䜙䜜䜛䚹䛭䛣䛷䠈ATP Ꮡᅾୗཪ䛿㠀Ꮡᅾୗ䛻䛚䛡䜛

GroES

䛸䛾┦஫స⏝䛾ゎᯒ䜢⾜䛳䛯䚹ᅗ

2-12

䛻䛚䛔䛶

ATP

Ꮡᅾୗཪ䛿㠀Ꮡᅾୗ䛻䛚䛡䜛

SR-1 G192I

GroES

䛾┦஫స⏝ゎᯒ⤖ᯝ䜢♧䛧䛯䚹䛣䛾䜾 䝷䝣䜘䜚ྛ䜹䜲䝛䝔䜱䝑䜽䝟䝷䝯䞊䝍䞊䛾⟬ฟ䜢⾜䛳䛯(⾲

2-2)䚹䛣䛾䝟䝷䝯䞊䝍䞊䛻䛚䛔䛶䠈SR-1 G2-2)䚹䛣䛾䝟䝷䝯䞊䝍䞊䛻䛚䛔䛶䠈SR-192I

ኚ␗య䛿

ATP

䛾᭷↓䛻㛵䜟䜙䛪

GroES

䛸䛾┦஫స⏝䛻ኚ໬䛿䜏䜙䜜䛺䛛䛳䛯䚹

63

GroEL G192W

ኚ␗య䛾

SPR

䛾⤖ᯝ䛸ẚ㍑䛧䛶

SR-1 G192䊠ኚ␗య䛿ゎ㞳ᐃᩘ K d

䛜 ⴭ䛧䛟ᑠ䛥䛔䛣䛸䛛䜙

GroES

䛜ゎ㞳䛧䜔䛩䛔䛣䛸䛜☜ㄆ䛷䛝䜛䚹SR-1 䛻䛚䛡䜛ᵝ䚻䛺㒊఩䛷 䛾Ⅼኚ␗䛿䛭䛾ศᏊ㔞䛻㐪䛔䛜⏕䛨䜛䚹䛣䜜䜙䛾ኚ␗య䛿

ATP

䛾Ꮡᅾୗ䛷䛾

GroES

䛾⤖

ྜ䛜኱䛝䛟ῶᑡ䛧䛶䛔䜛䛜䠈mtMDH 䛾䝸䝣䜷䞊䝹䝕䜱䞁䜾௓ຓ⬟ຊ䜢ಖᣢ䛧䛶䛔䜛䜒䛾䜒ሗ

࿌䛥䜜䛶䛔䜛

(95,96)

䚹䛣䛾䜘䛖䛻䠈

SR-1 G192X

ኚ␗య䛿䠈

SR-1 WT

䛸ẚ㍑䛧䠈

Gly192

ṧᇶ 䜢ኚ໬䛥䛫䛯䛣䛸䛷

GroES

䛸䛾┦஫స⏝䛜పୗ䛧䠈䛭䛾⤖ᯝ

MDH

䛾䝸䝣䜷䞊䝹䝕䜱䞁䜾䜢

⾜䛖䛣䛸䛜ྍ⬟䛻䛺䛳䛯䛸⪃䛘䜙䜜䜛䚹䛥䜙䛻䠈SR-1 䛻䛚䛡䜛

Gly192

䜢⨨᥮䛧䛯䜰䝭䝜㓟ṧᇶ 䛻䜘䜚

MDH

䛾䝸䝣䜷䞊䝹䝕䜱䞁䜾άᛶ䛻㐪䛔䛜䜏䜙䜜䛯䛣䛸䛛䜙䠈

SR-1 G192X

ኚ␗య䛿

GroES

䛸䛾┦஫స⏝䛾ᙉ䛥䛿

Gly192

䜢⨨᥮䛩䜛䜰䝭䝜㓟ṧᇶ䛻䜘䜚ኚ໬䛩䜛䛸⪃䛘䜙䜜䜛䚹 䛣䛾ᛶ㉁䛿䝎䝤䝹䝸䞁䜾䛾

GroEL

䛻䛚䛡䜛

cis

䉄ringഃ䛻㢮ఝ䛧䛯ᛶ㉁䛜཯ᫎ䛥䜜䛶䛔䜛䚹䛣 䛾

SR-1 G192X

ኚ␗య䜢⏝䛔䛯ゎᯒ䛻䜘䜚䠈ATP 㠀Ꮡᅾୗ䛻䛚䛡䜛

GroEL G192X

ኚ␗

య䛾

cis -ring

䛻䛚䛔䛶䠈⨨᥮䛧䛯䜰䝭䝜㓟ṧᇶ䛻䜘䛳䛶䛿᏶඲䛺

Open

≧ែ䜢䛸䛳䛶䛔䛺䛔 䛯䜑䛻

GroES

䛸䛾┦஫స⏝䛜ᙅ䛔䛸⪃䛘䜙䜜䜛䚹䜎䛯䠈7 䛴䛾

GroEL

䝃䝤䝴䝙䝑䝖䛻ᑐ䛧䛶

GroES

䛾䝃䝤䝴䝙䝑䝖䛜඲䛶⤖ྜ䛧䛶䛚䜙䛪䠈GroEL-GroES䛾᥋ゐ㠃䛻䛚䛔䛶㝽㛫䛜⏕䛨䠈 䛭䛣䛛䜙ᇶ㉁䛜እ䛻ᨺฟ䛥䜜䜛䛣䛸䜒⪃䛘䜙䜜䜛䚹

௨ୖ䛾䛣䛸䜘䜚䠈Gly192 䜢⨨᥮䛩䜛䜰䝭䝜㓟ṧᇶ䜢䜘䜚㑅ᢥⓗ䛻䛩䜛䛣䛸䛷䜰䝢䜹䝹䝗䝯䜲䞁 䛾

Open

䛺≧ែ䛜ไᚚ䛥䜜䠈䛭䜜䛻క䛖

GroES

䛸䛾┦஫స⏝䜔ኚᛶᇶ㉁䛾䝸䝣䜷䞊䝹䝕䜱䞁 䜾௓ຓ➼䛾䝅䝱䝨䝻䝙䞁䛸䛧䛶䛾ᶵ⬟䜢ㄪ⠇䛩䜛䛣䛸䛜ྍ⬟䛷䛒䜛䛣䛸䛜♧၀䛥䜜䛯䚹

64

➨ 3 ❶ GroEL Gly192 ኚ␗య䛻䜘䜛䜰䝭䝻䜲䝗⥺⥔จ㞟䛾

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