∞ÏÏËÏÔÁÚ·Ê›·: ƒ›ÌÈÓÈ 1, 12462 ÷˚‰¿ÚÈ ∆ËÏ.: 210-5831000, ÂÛˆÙ. 2214 e-mail: [email protected] ∫·Ù·Ù¤ıËΠ10.4.2005 ŒÁÈÓ ‰ÂÎÙ‹ 25.4.2005 Ã. ∫·ÏÏÈÓÙ¤ÚË, ¢. ∫·ÛÛ¿ÓÔ˜, ∂. ™·Ï·Ì·Ï¤Î˘. °’ ª·È¢ÙÈ΋ Î·È °˘Ó·ÈÎÔÏÔÁÈ΋ ∫ÏÈÓÈ΋ ¶·ÓÂÈÛÙËÌ›Ô˘ ∞ıËÓÒÓ, ¶.°.¡. «∞∆∆π∫√¡».
µÏ¿‚˜ ÙÔ˘ ÔÈÛı›Ô˘
‚fiıÚÔ˘ –Dandy Walker
Û‡Ó‰ÚÔÌÔ
¶ÂÚ›ÏË„Ë
To Û‡Ó‰ÚÔÌÔ Dandy Walker ·ÚÔ˘ÛÈ¿˙ÂÙ·È ÌÂ: 1) ‰È·ÊfiÚÔ˘ ‚·ı-ÌÔ‡ ‰È¿Ù·ÛË ÙˆÓ ÎÔÈÏÈÒÓ ÙÔ˘ ÂÁÎÂÊ¿ÏÔ˘, 2) ‰È·ÙÂٷ̤ÓË ÌÂÁ¿ÏË ‰ÂÍ·ÌÂÓ‹ Î·È 3) ¤ÏÏÂÈÌÌ· ÛÙÔ ÛÎÒÏËη Ù˘ ·ÚÂÁÎÂÊ·Ï›‰Ô˜ ̤-Ûˆ ÙÔ˘ ÔÔ›Ô˘ Ë ÌÂÁ¿ÏË ‰ÂÍ·ÌÂÓ‹ ÂÈÎÔÈÓˆÓ› Ì ÙËÓ Ù¤Ù·ÚÙË ÎÔÈÏ›·. ŒÓ· ¢ڇ Ê¿ÛÌ· ·ÓˆÌ·ÏÈÒÓ ÙÔ˘ Ô›ÛıÈÔ˘ ‚fiıÚÔ˘ ¤¯ÂÈ ÂÚÈÁÚ·Ê› ¯ˆÚ›˜ Ó· ˘¿Ú¯Ô˘Ó Û·Ê‹ ÎÚÈÙ‹ÚÈ· ‰È¿ÎÚÈÛ˘ ÌÂٷ͇ ÙÔ˘˜: 1) Ë ÎÏ·ÛÛÈ΋ Dandy Walker ·ÓˆÌ·Ï›· Ô˘ Û˘Ó›ÛÙ·Ù·È Û ‰È¿Ù·ÛË ÙÔ˘ Ô›ÛıÈÔ˘ ‚fiıÚÔ˘, Ï‹ÚË ‹ ÌÂÚÈ΋ ·ÁÂÓÂÛ›· ÙÔ˘ ÛÎÒÏËη Ù˘ ·ÚÂÁÎÂÊ·Ï›‰·˜ Î·È ·Ó˘„ˆÌ¤ÓÔ ÛÎËÓ›‰ÈÔ, 2) Ë ·-Ú·ÏÏ·Á‹ ÙÔ˘ Dandy Walker Ô˘ ÂÌÊ·Ó›˙ÂÈ ÔÈΛÏË ˘ÔÏ·Û›· ÙÔ˘ ÛÎÒÏËη Ù˘ ·ÚÂÁÎÂÊ·Ï›‰·˜ Ì ‹ ¯ˆÚ›˜ ‰È¿Ù·ÛË ÙÔ˘ Ô›-ÛıÈÔ˘ ‚fiıÚÔ˘), 3) Ë ‰È·ÙÂٷ̤ÓË ÌÂÁ¿ÏË ‰ÂÍ·ÌÂÓ‹ Ì ·Î¤Ú·ÈÔ ÙÔ ÛÎÒÏËη Î·È ÙËÓ Ù¤Ù·ÚÙË ÎÔÈÏ›·. ∂›Û˘ ¤¯ÂÈ ÂÚÈÁÚ·Ê› Ë ÔÈÎÔÁÂÓ‹˜ ·ÁÂÓÂÛ›· ÙÔ˘ ÛÎÒÏËη Ù˘ ·ÚÂÁÎÂÊ·Ï›‰·˜ ,ÙÔ Û‡Ó‰ÚÔÌÔ Joubert Ô˘ Û˘Óԉ‡ÂÙ·È ·fi ÂÂÈÛfi‰È· ˘ÂÚηӛ·˜, ·ıÔÏÔÁÈΤ˜ ÎÈÓ‹ÛÂȘ ÙˆÓ ÔÊı·ÏÌÒÓ ·Ù·Í›· Î·È ÓÔËÙÈ΋ ˘ÛÙ¤ÚËÛË. Èڛ˜ ÔÈÎÔÁÂÓ¤˜ ÈÛÙÔÚÈÎfi ÙÔ Û‡Ó-‰ÚÔÌÔ Joubert ‰ÂÓ ÌÔÚ› Ó· ‰È·ÎÚÈı› ·fi ÌÂÌÔӈ̤ÓË Dandy Walker ‰È·Ù·Ú·¯‹. ∏ ·ÓˆÌ·Ï›· Arnold Chiari Â›Ó·È Â›Û˘ ‚Ï¿‚Ë ÙÔ˘ ÔÈÛı›Ô˘ ÂÁÎÂÊ¿ÏÔ˘ Î·È ·ÔÙÂÏÂ›Ù·È ·fi ‰‡Ô ÛΤÏË. ∆Ô ÚÒÙÔ Â›Ó·È ‰È·-ÊfiÚÔ˘ ‚·ıÌÔ‡ ÌÂÙ·ÙfiÈÛË ÈÛÙÔ‡ Ô˘ ÚÔ¤Ú¯ÂÙ·È ·fi ÙÔ Î·ÙÒÙÂ-ÚÔ Ù̷̋ ÙÔ˘ ÛÎÒÏËη Ù˘ ·ÚÂÁÎÂÊ·Ï›‰·˜ ÛÙÔ ÛÔÓ‰˘ÏÈÎfi·˘-Ïfi. ∆Ô ‰Â‡ÙÂÚÔ Â›Ó·È Ì›· fiÌÔÈ· Ô˘Ú·›· ÌÂÙ·ÙfiÈ-ÛË Ù˘ Á¤Ê˘Ú·˜, Ù˘ ٤ٷÚÙ˘ ÎÔÈÏ›·˜ Î·È ÙÔ˘ ÚÔÌ‹ÎË Ì˘ÂÏÔ‡ ‰È·Ì¤ÛÔ˘ ÙÔ˘ ÈÓÈ·ÎÔ‡ ÙÚ‹Ì·ÙÔ˜ ÛÙÔ ÛÔÓ‰˘ÏÈÎfi ·˘Ïfi. ™˘Ó‹ıˆ˜ Û˘Óԉ‡ÂÙ·È Ì ˘‰ÚÔΤʷÏÔ Î·È ÌËÓÈÁÁÔÌ˘ÂÏÔ΋ÏË. §¤ÍÂȘ-ÎÏÂȉȿ: Û‡Ó‰ÚÔÌÔ Dandy Walker, ·ÓˆÌ·Ï›Â˜ ‰È¿-Ï·Û˘ ÙÔ˘ ÛÎÒÏËη, ‰È¿Ù·ÛË Ù˘ ÙÂÙ¿ÚÙ˘ ÎÔÈÏ›·˜ ∂ÈÛ·ÁˆÁ‹ – ∞Ó·ÙÔÌ›· ∆Ô Û‡Ó‰ÚÔÌÔ Dandy Walker ÂÚÈÏ·Ì‚¿ÓÂÈ ÌÈ· ÛÂÈÚ¿ ·ÓˆÌ·ÏÈÒÓ ÔÈ Ôԛ˜ ÔÊ›ÏÔÓÙ·È Û ·ıÔÏÔÁÈ΋ ·Ó¿Ù˘ÍË Ù˘ ·ÚÂÁÎÂÊ·Ï›-‰·˜ . ∆Ô Û‡Ó‰ÚÔÌÔ ·˘Ùfi Â›Ó·È ·ÔÙÂÏ› ¤Ó· Ê¿ÛÌ· ‰È·Ù·Ú·¯ÒÓ Ô˘ ÚÔ·ÙÔ˘Ó ·fi ÙËÓ ˘Ô-Ï·Û›· Ù˘ ·ÚÂÁÎÂÊ·Ï›‰·˜ Î·È ÙË Û˘ÓÔ‰fi η΋ ·Ó¿Ù˘ÍË Ù˘ ٤ٷÚÙ˘ ÎÔÈÏ›·˜. ∫˘Ú›·Ú-¯Ô ‡ÚËÌ· Â›Ó·È Ë ÌÂÁ¿ÏË ‰È¿Ù·ÛË Ù˘ ٤ٷÚ-Ù˘ ÎÔÈÏ›·˜ ÙÔ˘ ÂÁÎÂÊ¿ÏÔ˘ ,Ë ÔÔ›· ÌÂÁ·ÏÒ-ÓÂÈ ÙfiÛÔ Ôχ ÒÛÙ ηٷϷ̂¿ÌÂÁ·ÏÒ-ÓÂÈ Î·È ‰È·Ù›-ÓÂÈ ÙÔÓ Ô›ÛıÈÔ ‚fiıÚÔ. ™˘Ó‰˘¿˙ÂÙ·È Ì ‰È·ÊfiÚÔ˘ ‚·ıÌÔ‡ ‰È¿Ù·ÛË ÙˆÓ Ï·Á›ˆÓ ÎÔÈÏÈÒÓ Ì ‰È·ÙÂٷ̤ÓË ÌÂÁ¿ÏË ‰ÂÍ·ÌÂÓ‹ Î·È ¤ÏÏÂÈÌÌ· ÙÔ˘ ÛÎÒÏËη Ù˘ ·-ÚÂÁÎÂÊ·Ï›‰·˜ ̤ۈ ÙÔ˘ ÔÔ›Ô˘ Ë ÌÂÁ¿ÏË ‰Â-Í·ÌÂÓ‹ ÂÈÎÔÈÓˆÓ› Ì ÙËÓ Ù¤Ù·ÚÙË ÎÔÈÏ›·.1 ∆· ÙÂÏÂ˘Ù·›· ¯ÚfiÓÈ· ‰È¿ÊÔÚÔÈ ÔÚÈÛÌÔ› ¤¯Ô˘Ó ÚÔÙ·ı› ÁÈ· Ó· ‰ËÏÒÛÔ˘Ó ÙËÓ ÔÌ¿‰· ÙˆÓ ·ÓˆÌ·ÏÈÒÓ ÙÔ˘ Ô›ÛıÈÔ˘ ‚fiıÚÔ˘ Ô˘ ÌÔÈ¿-˙Ô˘Ó Ì ÙÔ ÎÏ·ÛÛÈÎfi Û‡Ó‰ÚÔÌÔ Dandy Walker. √È ÂÚÈÛÛfiÙÂÚÔÈ ÔÚÈÛÌÔ› ÂÚÈÏ·Ì‚¿ÓÔ˘Ó Ù· ·ÎfiÏÔ˘ı· Â˘Ú‹Ì·Ù·: 1) ΢ÛÙÈ΋ ‰È¿Ù·ÛË Ù˘ ٤ٷÚÙ˘ ÎÔÈÏ›·˜ ,2) ‰˘ÛÁÂÓÂÛ›· ÙÔ˘ ÛÎÒÏËη Ù˘ ·ÚÂÁÎÂÊ·Ï›‰·˜ Î·È 3) ˘„ËÏ‹ ı¤ÛË ÙÔ˘ ÛÎËÓȉ›Ô˘. ∂› ÙÔ˘ ·ÚfiÓÙÔ˜, Ô fiÚÔ˜ Dandy Walker ¯ÚËÛÈÌÔÔÈÂ›Ù·È ÁÈ· Ó· ‰Â›ÍÂÈ ¤Ó· Ê¿ÛÌ· ·ÓˆÌ·ÏÈÒÓ ÙÔ˘ Ô›ÛıÈÔ˘ ‚fiıÚÔ˘ ÔÈ Ôԛ˜ Ù·ÍÈÓÔÌÔ‡ÓÙ·È ·fi ÙËÓ ·ÍÔÓÈ΋ ˘Ô-ÏÔÁÈÛÙÈ΋ ÙÔÌÔÁÚ·Ê›· (CT scans) ˆ˜ ·ÎÔÏÔ‡-ıˆ˜: 1) ÎÏ·ÛÛÈ΋ Dandy Walker ·ÓˆÌ·Ï›·, (‰È¿Ù·ÛË ÙÔ˘ Ô›ÛıÈÔ˘ ‚fiıÚÔ˘, Ï‹Ú˘ ‹ ÌÂ-ÚÈ΋ ·ÁÂÓÂÛ›· ÙÔ˘ ÛÎÒÏËη Ù˘ ·ÚÂÁÎÂÊ·-Ï›‰·˜, ·Ó˘„ˆÌ¤ÓÔ ÛÎËÓ›‰ÈÔ) 2) ·Ú·ÏÏ·Á‹ ÙÔ˘ Dandy Walker (ÔÈΛÏË ˘ÔÏ·Û›· ÙÔ˘ ÛÎÒÏËη Ù˘ ·ÚÂÁÎÂÊ·Ï›‰·˜ Ì ‹ ¯ˆÚ›˜ ‰È¿Ù·ÛË ÙÔ˘ Ô›ÛıÈÔ˘ ‚fiıÚÔ˘) Î·È 3) ‰È·ÙÂ-ٷ̤ÓË ÌÂÁ¿ÏË ‰ÂÍ·ÌÂÓ‹ Ì ·Î¤Ú·ÈÔ ÙÔ ÛÎÒ-ÏËη Î·È ÙËÓ Ù¤Ù·ÚÙË ÎÔÈÏ›· (mega-cisterna magna).2 ∞Ó Î·È Ô ˘‰ÚÔΤʷÏÔ˜ ¤¯ÂÈ ıˆÚËı› fiÙÈ Â›-Ó·È ¤Ó· Ô˘ÛÈ·ÛÙÈÎfi ‰È·ÁÓˆÛÙÈÎfi ÛÙÔÈ¯Â›Ô ÛÙÔ Û‡Ó‰ÚÔÌÔ Dandy Walker, ÈÔ ÚfiÛÊ·Ù˜ ÌÂ-ϤÙ˜ ·Ó·Ê¤ÚÔ˘Ó fiÙÈ Î·È ÛÙÔ ÎÏ·ÛÛÈÎfi Û‡Ó-‰ÚÔÌÔ Ë ‰È¿Ù·ÛË ÙˆÓ ÎÔÈÏÈÒÓ ‰ÂÓ Â›Ó·È Úˆ-Ù·Ú¯ÈÎfi ‡ÚËÌ· ηٿ ÙË Á¤ÓÓËÛË ÛÙÔ˘˜ Â-ÚÈÛÛfiÙÂÚÔ˘˜ ·ÛıÂÓ›˜ ·ÏÏ¿ ·Ó·Ù‡ÛÛÂÙ·È Û˘¯Ó¿ ÙÔ˘˜ ÚÒÙÔ˘˜ ̋Ә Ù˘ ˙ˆ‹˜.3 ∏ ·ÓˆÌ·Ï›· Dandy Walker ÂÌÊ·Ó›˙ÂÙ·È ÌÂ Û˘¯ÓfiÙËÙ· 1/ 30000 ÁÂÓÓ‹ÛÂȘ Î·È Â˘Ú›ÛÎÂÙ·È Û 4% ¤ˆ˜ 12% fiÏˆÓ ÙˆÓ ÂÚÈÙÒÛÂˆÓ ÓÂÔ-ÁÓÈÎÔ‡ ˘‰ÚÔΤʷÏÔ˘. ∏ Û˘¯ÓfiÙËÙ· ÙˆÓ ·-Ú·ÏÏ·ÁÒÓ ÙÔ˘ Û˘Ó‰ÚfiÌÔ˘ Î·È Ù˘ ‰È·ÙÂٷ̤-Ó˘ ÌÂÁ¿Ï˘ ‰ÂÍ·ÌÂÓ‹˜ Â›Ó·È ¿ÁÓˆÛÙË. £Âˆ-ڛ˜ ÁÈ· ÙËÓ ·ıÔÁ¤ÓÂÛË ÂÚÈÏ·Ì‚¿ÓÔ˘Ó ·ÙÚËÛ›· ÙˆÓ ÙÚËÌ¿ÙˆÓ Luschka Î·È Magendie ·Ó Î·È ·˘Ù¿ ÌÔÚ› Ó· ·ÚÔ˘ÛÈ¿-˙Ô˘Ó Î¿ÔÈ· ‰È·‚·ÙfiÙËÙ· Î·È Ê·›ÓÂÙ·È Ó· ˘¿Ú¯ÂÈ ˘ÔÏ·Û›· Î·È Î¿ÔÈÔ˘ ‚·ıÌÔ‡ ·-ıÔÏÔÁÈ΋ ·Ó¿Ù˘ÍË Ù˘ ·ÚÂÁÎÂÊ·Ï›‰·˜.4 º·›ÓÂÙ·È fiÙÈ ÛÙËÓ ·ÈÙ›· ·˘Ù‹˜ Ù˘ ηٿÛÙ·-Û˘ ·›˙Ô˘Ó ÛËÌ·ÓÙÈÎfi ÚfiÏÔ ÁÂÓÂÙÈÎÔ› ·Ú¿-ÁÔÓÙ˜. ∏ ·ÓˆÌ·Ï›· Dandy Walker ÌÔÚ› Ó· ÔÊ›ÏÂÙ·È Û ÌÂÓÙÂÏÈΤ˜ ‰È·Ù·Ú·¯¤˜ Î·È Û ¯ÚˆÌ·ÙÔۈ̷ÙÈΤ˜ ÌÂÙ·ÏÏ¿ÍÂȘ ∂¿Ó ‰ÂÓ ·ÔÙÂÏ› ̤ÚÔ˜ ·Ó·ÁÓˆÚÈṲ̂ÓÔ˘ Û˘Ó‰ÚfiÌÔ˘, Ô Î›Ó‰˘ÓÔ˜ ·ÓÂÌÊ¿ÓÈÛ˘ Â›Ó·È 1% ¤ˆ˜ 5%.™Â Û¿ÓȘ ÂÚÈÙÒÛÂȘ Ë ·Ûı¤ÓÂÈ· ÎÏË-ÚÔÓÔÌÂ›Ù·È Ì ·˘ÙÔۈ̷ÙÈÎfi ˘ÔÏÂÈfiÌÂÓÔ ÙÚfiÔ.5 ¶ÂÚÈ‚·ÏÏÔÓÙÈÎÔ› ·Ú¿ÁÔÓÙ˜, ÊÏÂÁÌÔÓ¤˜ ·fi ÈÔ‡˜, Ï‹„Ë ·ÏÎÔfiÏ Î·È ‰È·‚‹Ù˘ Ù˘ ÌËÙ¤Ú·˜ ¤¯Ô˘Ó ÂÓÔ¯ÔÔÈËı› ÁÈ· ÙËÓ ÂÌÊ¿ÓÈÛË ÙÔ˘ Û˘Ó‰ÚfiÌÔ˘. ∏ Ù·ÍÈÓfiÌËÛË ÙÔ˘ Û˘Ó‰ÚfiÌÔ˘ ¤ÁÈÓ ηχÙÂÚË Ì ÙËÓ ÂÊ·ÚÌÔÁ‹ ÙÔ˘ MRI. °È· ‰È·ÊfiÚÔ˘˜ ÏfiÁÔ˘˜ ÔÈ ·ÏÏ¿ÏÏËϘ ÙÔ̤˜ Ô˘ ·Ú·‰ÔÛȷο ¯ÚËÛÈÌÔÔÈÔ‡ÓÙ·È ÛÙËÓ CT ‰ÂÓ ¤¯Ô˘Ó ÙËÓ ÈηÓfiÙËÙ· Ó· ÂÎÙÈÌ‹ÛÔ˘Ó Ì ·ÎÚ›‚ÂÈ· ÙÔ Ì¤ÁÂıÔ˜ ÙÔ˘ ÛÎÒÏËη Ù˘ ·ÚÂ-ÁÎÂÊ·Ï›‰·˜ Î·È ÌÔÚÔ‡Ó Ó· ˘ÔÂÎÙÈÌ‹ÛÔ˘Ó ‹ Ó· ˘ÂÚÂÎÙÈÌ‹ÛÔ˘Ó ÙÔ Ì¤ÁÂıÔ˜ ÂÓfi˜ ÂÏÏ›Ì-Ì·ÙÔ˜. ∏ ÂÍ·ÈÚÂÙÈ΋ ·Ó¿Ï˘ÛË ÙˆÓ ÂÈ̋ΈÓ
ÂȤ-‰ˆÓ Ô˘ ÂÈÙ‡¯ıËΠ̠ÙËÓ MRI ·¤‰ÂÈÍ fiÙÈ Ë Ù·ÍÈÓfiÌËÛË Ô˘ ¤ÁÈÓ Ì ÙËÓ CT ‹Ù·Ó ·Ó·Ú΋˜ Ó· ÂÚÈÁÚ¿„ÂÈ ÙËÓ ·Ó·ÙÔÌÈ΋ ‰È·-Ù·Ú·¯‹ ÙÔ˘ Û˘Ó‰ÚfiÌÔ˘ Dandy Walker. ∫¿-ÔÈÔÈ ‚·ıÌÔ› ‰˘ÛÁÂÓÂÛ›·˜ ÙÔ˘ ÛÎÒÏËη ÌÔ-ÚÔ‡Ó Ó· ¢ÚÂıÔ‡Ó Û fiϘ ÙȘ ÂÚÈÙÒÛÂȘ, ·ÎfiÌË Î·È fiÙ·Ó ˘¿Ú¯ÂÈ ÌÂÁ¿ÏË ‰È¿Ù·ÛË Ù˘ ÌÂÁ¿Ï˘ ‰ÂÍ·ÌÂÓ‹˜, ÂÓÒ Ë ÎÏ·ÛÛÈ΋ ÌÔÚÊ‹ Î·È ÔÈ ·Ú·ÏÏ·Á¤˜ ÙÔ˘ Û˘Ó‰ÚfiÌÔ˘ ¤¯Ô˘Ó Ùfi-Û˜ ÔÌÔÈfiÙËÙ˜ Ô˘ ¤Ó·˜ Û·Ê‹˜ ‰È·¯ˆÚÈÛÌfi˜ ÌÔÚ› Ó· Â›Ó·È ·‰‡Ó·ÙÔ˜. To Û‡Ó‰ÚÔÌÔ ·˘Ùfi ÌÔÚ› Ó· Û˘Óԉ‡ÂÙ·È Û˘¯Ó¿ Î·È Ì ¿ÏϘ ‚Ï¿‚˜ ÙÔ˘ ¡Â˘ÚÈÎÔ‡ ™˘-ÛÙ‹Ì·ÙÔ˜ ΢ڛˆ˜ ‰È¿Ù·ÛË ÙˆÓ ÎÔÈÏÈÒÓ, Î·È ‚Ï¿‚˜ Ù˘ ̤Û˘ ÁÚ·ÌÌ‹˜, fiˆ˜ ·ÁÂÓÂÛ›· ÙÔ˘ ÌÂÛÔÏÔ‚›Ô˘, ÔÏÔÚÔÛÂÁÎÂÊ·Ï›· Î·È ÂÁÎÂÊ·ÏÔ΋Ϙ. ™Â ·ÚÎÂÙ¤˜ ÂÚÈÙÒÛÂȘ ¤¯ÂÈ ÂÚÈÁÚ·Ê› Ë ·ÚÔ˘Û›· ÔÏ˘‰·ÎÙ˘Ï›·˜, ·Óˆ-Ì·ÏÈÒÓ ÙÔ˘ Ô˘ÚÔÔÈËÙÈÎÔ‡ Û˘ÛÙ‹Ì·ÙÔ˜, ηÚ-‰È·ÁÁÂȷΤ˜ ·ÓˆÌ·Ï›Â˜ Î·È Û¯ÈÛٛ˜ ÙÔ˘ ÚÔ-ÛÒÔ˘.6 ªÂϤÙ˜ ÌÂÙ¿ ÙË Á¤ÓÓËÛË ÂÌÊ·Ó›˙Ô˘Ó Û˘¯Ófi-ÙËÙ· Û˘ÓÔ‰ÒÓ ·ÓˆÌ·ÏÈÒÓ Ô˘ Î˘Ì·›ÓÔÓÙ·È ÌÂٷ͇ 50% Î·È 70%. ÀÂÚ˯ÔÁÚ·Ê›· ∏ ˘ÂÚ˯ÔÁÚ·ÊÈ΋ ‰È¿ÁÓˆÛË ÙÔ˘ ÎÏ·ÛÛÈÎÔ‡ Dandy Walker Â›Ó·È ‰˘Ó·Ù‹ Û˘Ó‹ıˆ˜ ·fi ÙÔ 2Ô ÙÚ›ÌËÓÔ Ù˘ ÂÁ΢ÌÔÛ‡Ó˘7 fï˜ ¤¯ÂÈ ·Ó·-ÊÂÚı› Î·È ·fi ÙË 14Ë Â‚‰ÔÌ¿‰· Ù˘ ·ËÛ˘ ¯ÚËÛÈÌÔÔÈÒÓÙ·˜ ‰È·ÎÔÏÈ΋ ˘ÂÚ˯ÔÁÚ·-Ê›·.8 ™Â ˘ÈÓÈÔ‚ÚÂÁÌ·ÙÈ΋ ÙÔÌ‹, Ô˘ Ê·›ÓÂÙ·È Ë ·ÚÂÁÎÂÊ·Ï›‰·, ˘ÂÚ˯ÔÁÚ·ÊÈο ‰È·ÈÛÙÒ-ÓÂÙ·È Ì›· ‰È·ÙÂٷ̤ÓË Ô›ÛıÈ· ‰ÂÍ·ÌÂÓ‹ Ô˘ ÂÈÎÔÈÓˆÓ› Ì ÙËÓ ÂÚÈÔ¯‹ Ù˘ ٤ٷÚÙ˘ ÎÔÈ-Ï›·˜ ̤ۈ ÂÏÏ›ÌÌ·ÙÔ˜ ÙÔ˘ ·ÚÂÁÎÂÊ·ÏȉÈ-ÎÔ‡ ÛÎÒÏËη (∂ÈÎfiÓ· 1) ™˘¯Ó¿ ÌÔÚ› Ó· ·Ó¢ÚÂıÔ‡Ó ÔÚȷ΋ ̤¯ÚÈ ÂÎÙÂٷ̤ÓË ÎÔÈÏÈÔ-ÌÂÁ·Ï›· Î·È ¿ÏϘ ‚Ï¿‚˜ ·fi ÙÔ ÎÂÓÙÚÈÎfi Ó¢ÚÈÎfi Û‡ÛÙËÌ· ηıÒ˜ Î·È Û˘ÓÔ‰¤˜ ‰È·Ù·-Ú·¯¤˜ ·fi ¿ÏÏ· Û˘ÛÙ‹Ì·Ù·. ∂ÓÙÔ‡ÙÔȘ Û ÂÚÈÙÒÛÂȘ Ì ÌÂÚÈ΋ ·ÁÂÓÂ-Û›· ÙÔ˘ ÛÎÒÏËη ÛÙÔ Î·ÙÒÙÂÚÔ ÙÔ˘ Ù̷̋ ,Ë ÎÏ·ÛÛÈ΋ ÙÔÌ‹ Ô˘ ÂÚÈÏ·Ì‚¿ÓÂÈ ÙËÓ ·ÚÂ-ÁÎÂÊ·Ï›‰· ÌÔÚ› Ó· ÌËÓ Â›Ó·È ‰È·ÁÓˆÛÙÈ΋ Î·È Ó· ··ÈÙËı› ›ÌÔÓË ‰ÈÂÚ‡ÓËÛË ÁÈ· Ó· ‰È·ÈÛÙˆı› ÙÔ ¤ÏÏÂÈÌÌ·. ÃÚÂÈ¿˙ÂÙ·È ‰ËÏ·‰‹ ¤ÏÂÁ¯Ô˜ Ì ̛· ¯·ÌËÏfiÙÂ-ÚË ÙÔÌ‹ ÁÈ· Ó· ·Ô‰ÂȯÙ› fiÙÈ ÙÔ Î·ÙÒÙÂÚÔ Ù̷̋ ÙÔ˘ ÛÎÒÏËη ¯ˆÚ›˙ÂÈ ÙËÓ Ù¤Ù·ÚÙË ÎÔÈ-Ï›· ·fi ÙËÓ ÌÂÁ¿ÏË ‰ÂÍ·ÌÂÓ‹ Î·È Ó· ·Ô-ÎÏÂÈÛÙ› ¤ÙÛÈ ·˘Ù‹ Ë Î·Ù¿ÛÙ·ÛË.9 ∫ÚÈÙ‹ÚÈ· ÁÈ· ÔÚÈÛÙÈ΋ ‰È¿ÁÓˆÛË Ù˘ ‰È·ÙÂÙ·-̤Ó˘ ÌÂÁ¿Ï˘ ‰ÂÍ·ÌÂÓ‹˜ Î·È ÙˆÓ ·Ú·ÏÏ·-ÁÒÓ Dandy Walker ‰ÂÓ ¤¯Ô˘Ó ·˘ÛÙËÚ¿ ηıÔ-ÚÈÛÙ› ̤¯ÚÈ ÙÒÚ·.10 ∆ËÓ ‰È·ÙÂٷ̤ÓË ÌÂÁ¿ÏË ‰ÂÍ·ÌÂÓ‹ Ú¤ÂÈ Ó· ÙËÓ ˘ÔÙ¢fiÌ·ÛÙ fiÙ·Ó ÙÔ ‚¿ıÔ˜ Ù˘ ÌÂÁ¿Ï˘ ‰ÂÍ·ÌÂÓ‹˜ Â›Ó·È ÌÂÁ·-χÙÂÚÔ ·fi10mm,11Î·È ÙËÓ ·Ú·ÏÏ·Á‹ ÙÔ˘ Û˘Ó‰ÚfiÌÔ˘ fiÙ·Ó Ì›· ÌÈÎÚ‹ ÂÈÎÔÈÓˆÓ›· ‚Ú›-ÛÎÂÙ·È ÌÂٷ͇ Ù˘ ٤ٷÚÙ˘ ÎÔÈÏ›·˜ Î·È Ù˘ ÌÂÁ¿Ï˘ ‰ÂÍ·ÌÂÓ‹˜. ™ÙȘ ·Ú¯¤˜ ÙÔ˘ 2Ô˘ ÙÚÈÌ‹ÓÔ˘ Ë ˘ÂÚ˯ÔÁÚ·-ÊÈ΋ ÂÌÊ¿ÓÈÛË Ê˘ÛÈÔÏÔÁÈ΋˜ ·Ó¿Ù˘Í˘ Ù˘ ∂ÈÎfiÓ· 1: ™‡Ó‰ÚÔÌÔ Dandy Walker. ¢ÂÓ ·Ú·ÙËÚÂ›Ù·È ·ÚÂÁÎÂÊ·Ï›‰· Û ˘ÈÓÈÔ‚ÚÂÁÌ·ÙÈ΋ ÙÔÌ‹ ∂ÈÎfiÓ· 2: ∞Á¤ÓÂÛË ÙÔ˘ ÛÎÒÏËη Î·È ˘‰ÚÔÎÂÊ·Ï›·
ÂÚÂÁÎÂÊ·Ï›‰·˜ ÌÔÚ› Ó· ÌËÓ ·Ôηχ„ÂÈ ÙË ÓfiÛÔ. ∏ Û¯ÂÙÈο ÌÂÁ¿ÏË Ù¤Ù·ÚÙË ÎÔÈÏ›· Î·È Ô ·ÓÂ-·Ú΋˜ Û¯ËÌ·ÙÈÛÌfi˜ ÙÔ˘ ÛÎÒÏËη ÌÔÚ› Ó· ‰ÒÛÔ˘Ó ÙËÓ ÂÛÊ·Ï̤ÓË ÂÓÙ‡ˆÛË ÙÔ˘ ÂÏÏ›Ì-Ì·ÙÔ˜ ÛÙÔ ÛÎÒÏËη .∂›Ó·È ÂÔ̤ӈ˜ ÚÒÈÌÔ Ó· οÓÂÈ Î·Ó›˜ ÙË ‰È¿ÁÓˆÛË Ù˘ ¤ÏÏÂȄ˘ ÙÔ˘ ÛÎÒÏËη Û ·˘Ù‹Ó ÙËÓ ËÏÈΛ· ·ËÛ˘. ™˘-ÓÈÛÙ¿Ù·È Â·Ó¿ÏË„Ë ÙÔ˘ ˘ÂÚ˯ÔÁڷʋ̷ÙÔ˜ ÛÙȘ 18 ‚‰ÔÌ¿‰Â˜ ‹ Î·È ·ÚÁfiÙÂÚ·. ∞ÎfiÌË Î·È ÛÙÔ 2Ô ‹ 3Ô ÙÚ›ÌËÓÔ Ì›· ÏÔÍ‹ ÎÏ›ÛË Ù˘ ÁˆÓ›·˜ Û¿ÚˆÛ˘ ÌÔÚ› Ó· ‰ÒÛÂÈ ÙËÓ ÂÓÙ‡-ˆÛË Ù˘ ·‡ÍËÛ˘ ÙÔ˘ ÌÂÁ¤ıÔ˘˜ Ù˘ ÌÂÁ¿Ï˘ ‰ÂÍ·ÌÂÓ‹˜, Î·È ÂÏÏ›ÌÌ·ÙÔ˜ ÙÔ˘ ÛÎÒÏËη.12 ∏ ·Ú¯‹ ÙÔ˘ Ù¯ÓÈÎÔ‡ ·˘ÙÔ‡ ÛÊ¿ÏÌ·ÙÔ˜ Â›Ó·È ·Û·Ê‹˜. Œ¯ÂÈ ˘ÔÙÂı› fiÙÈ ÌÔÚ› Ó· ‰ËÌÈ-Ô˘ÚÁËı› ·fi ÙËÓ ·ÚÔ˘Û›· ˘ÁÚÔ‡ ·Ó¿ÌÂÛ· ÛÙȘ ·‡Ï·Î˜ Ù˘ ·ÚÂÁÎÂÊ·Ï›‰·˜ Ô˘ Ù›ÓÂÈ Ó· ÂÂÎÙ·ı› ÚÔ˜ Ù· ÂÌÚfi˜ Î·È Î·Ï‡ÙÂÙ·È ·fi ¤Ó· ÏÂÙfi ÌÂ̂ڷÓ҉˜ Î¿Ï˘ÌÌ· ÙÔ ÔÔ›Ô ‰ÂÓ ÌÔÚ› Ó· Á›ÓÂÈ ·ÓÙÈÏËÙfi Ì ÙË ‰Â-‰Ô̤ÓË ·Ó¿Ï˘ÛË Ù˘ ÂÈÎfiÓ·˜ ·fi ÙÔÓ ˘¿Ú-¯ÔÓÙ· Ù¯ÓÔÏÔÁÈÎfi ÂÍÔÏÈÛÌfi. ∏ ·Ú·Î›ÌÂ-ÓË ı¤ÛË ÙˆÓ ·˘Ï¿ÎˆÓ Ù˘ ·ÚÂÁÎÂÊ·Ï›‰·˜, ‰ËÌÈÔ˘ÚÁ› ÙËÓ ÂÓÙ‡ˆÛË Ù˘ ÂÈÎÔÈÓˆÓ›·˜ ÌÂٷ͇ Ù˘ ٤ٷÚÙ˘ ÎÔÈÏ›·˜ Î·È Ù˘ ÌÂÁ¿Ï˘ ‰ÂÍ·ÌÂÓ‹˜, fiÌÔÈ· Ì ·˘Ù‹ Ô˘ ÂÚÈÁÚ¿ÊÂÙ·È Û CT ÌÂϤÙ˜ Ù˘ ·Ú·ÏÏ·Á‹˜ ÙÔ˘ Û˘Ó‰Úfi-ÌÔ˘ Dandy Walker. ∏ ÂÈÛÎfiËÛË ÙÔ˘ ÔÈ-Ûı›Ô˘ ‚fiıÚÔ˘ Û ̤ÛÔ Â›Â‰Ô ÌÔÚ› Ó· ‚ÔËı‹ÛÂÈ Û ·˘Ù¤˜ ÙȘ ÂÚÈÙÒÛÂȘ ÂÊfiÛÔÓ ÂÈÙÚ¤ÂÈ ÙËÓ ÂÈÛÎfiËÛË ÙÔ˘ ÛÎÒÏËη Ù˘ ·ÚÂÁÎÂÊ·Ï›‰·˜ Û ԂÂÏÈ·›Ô ›‰Ô.13 ∞ÎfiÌË Î·È ·˘Ù‹ Ë ÚÔÛ¤ÁÁÈÛË ÌÔÚ› Ó· ÌËÓ ÂÈÙÚ¤„ÂÈ ÙË Û·Ê‹ Ù·˘ÙÔÔ›ËÛË Ù˘ ‰˘ÛÁÂÓÂ-Û›·˜ Ù˘ ·ÚÂÁÎÂÊ·Ï›‰·˜. ªÂ ‚¿ÛË Ù· ‰Â‰Ô̤ӷ, ÙÔ ˘ÂÚ˯ÔÁÚ¿ÊËÌ· ÌÂÙ¿ ÙË Á¤ÓÓËÛË ÂÈÙÚ¤ÂÈ ÙË ‰È¿ÁÓˆÛË Ìfi-ÓÔÓ ÛÔ‚·ÚÒÓ ·Ó·ÙÔÌÈÎÒÓ ·Ú·ÏÏ·ÁÒÓ ÙÔ˘ Dandy Walker ·˘Ù¤˜ ÂÚÈÏ·Ì‚¿ÓÔ˘Ó ‰È·ÙÂÙ·-̤ÓË ÌÂÁ¿ÏË ‰ÂÍ·ÌÂÓ‹ Î·È ¤Ó· ¢ڇ ¤ÏÏÂÈÌÌ· ÙÔ˘ ·ÚÂÁÎÂÊ·ÏȉÈÎÔ‡ ÛÎÒÏËη Î·È ¯·Ú·-ÎÙËÚ›˙ÔÓÙ·È Û·Ó ÎÏ·ÛÛÈ΋ ‰È·Ù·Ú·¯‹ Dandy Walker. ∏ ÂÌÂÈÚ›· Â›Ó·È ÂÚÈÔÚÈṲ̂ÓË Ì ÏÈÁfiÙÂÚÔ Û·Ê›˜ ·Ú·ÏÏ·Á¤˜. ∂›Ó·È Û˘¯Ó¿ ·‰‡Ó·ÙÔ Ó· ‰È·ÁÓˆÛÙ› ÌÂÙ¿ ÙÔÓ ÙÔÎÂÙfi Â¿Ó ÚfiÎÂÈÙ·È ÁÈ· ÌÈ· ‰È·ÙÂٷ̤ÓË ÌÂÁ¿ÏË ‰ÂÍ·ÌÂÓ‹ ‹ ¤Ó· ÌÈÎÚfi ¤ÏÏÂÈÌÌ· ÛÙÔ ÛÎÒÏËη. ∏ ÎÏ·ÛÛÈ΋ ‰È·Ù·Ú·¯‹ Dandy Walker ÎÏÈÓÈ-ο ÂΉËÏÒÓÂÙ·È ÙÔÓ ÚÒÙÔ ¯ÚfiÓÔ Ù˘ ˙ˆ‹˜, ÌÂ Û˘ÌÙÒÌ·Ù· ˘‰ÚÔÎÂÊ¿ÏÔ˘ ‹ ¿ÏÏˆÓ Ó¢ÚÔ-ÏÔÁÈÎÒÓ ÛËÌ›ˆÓ. Œ¯ÂÈ ·Ó·ÊÂÚı› ˘„ËÏ‹ ıÓËÛÈÌfiÙËÙ· ¤ˆ˜ 24% ÛÙȘ ÚÒÙ˜ Ó¢ÚÔ¯ÂÈ-ÚÔ˘ÚÁÈΤ˜ ÌÂϤÙ˜, ·ÏÏ¿ ÏfiÁˆ ÙˆÓ ÂÍÂÏ›ÍÂˆÓ ÛÙËÓ ·È‰È·ÙÚÈ΋ ·Ó·ÈÛıËÛ›· Î·È ÛÙȘ ¯ÂÈ-ÚÔ˘ÚÁÈΤ˜ Ù¯ÓÈΤ˜ ÔÈ ı¿Ó·ÙÔÈ Û·ÊÒ˜ ¤¯Ô˘Ó Á›ÓÂÈ ÏÈÁfiÙÂÚÔÈ. ∏ ÓÂ˘Ì·ÙÈ΋ ·Ó¿Ù˘ÍË ÛÙÔ˘˜ ÂÈ˙‹Û·ÓÙ˜ Â›Ó·È ·ÌÊÈÏÂÁfiÌÂÓË. ¢Â‰Ô̤Ó˘ Ù˘ Û·ÓÈfi-ÙËÙ·˜ Ù˘ ηٿÛÙ·Û˘ ·˘Ù‹˜ ˘¿Ú¯Ô˘Ó ÌfiÓÔ ÂÚÈÔÚÈṲ̂Ó˜ ÌÂϤÙ˜. ¶·Ú ·˘Ù¿ ÂÏ·Ùو̤-ÓË ÓÔËÌÔÛ‡ÂÏ·Ùو̤-ÓË ·Ó·Ê¤ÚÂÙ·È Û 40 ¤ˆ˜ 70% ÙˆÓ ÂÚÈÙÒÛˆÓ. √È Ulm Î·È Û˘Ó.14 ÌÂϤÙËÛ·Ó ÙËÓ ˘fiıÂÛË fiÙÈ Ë ÚÒÈÌË ÂÓ‰ÔÌËÙÚÈ΋ ‰È¿-ÁÓˆÛË Â›Ó·È Èı·ÓfiÙÂÚÔ Ó· Û˘Óԉ‡ÂÙ·È Ì ÈÔ ÊÙˆ¯‹ ÚfiÁÓˆÛË. °È· ÙÔ ÛÎÔfi ·˘Ùfi Âͤ-Ù·Û·Ó ÛÂÈÚ¤˜ Ì ۇÁ¯ÚÔÓË ‰ÔÌÈ΋ Î·È ¯ÚˆÌÔ-ۈ̷ÙÈ΋ ·ÓˆÌ·Ï›· Û ¤Ì‚Ú˘· Ì Dandy Walker ‹ ·Ú·ÏÏ·Á‹˜ ÙÔ˘ Û˘Ó‰ÚfiÌÔ˘ ÚÈÓ ·fi ÙȘ 21 ‚‰ÔÌ¿‰Â˜ Ù˘ ·ËÛ˘ Û˘ÁÎÚÈÓfi-ÌÂÓ˜ Ì ¤Ì‚Ú˘· Ì ‰È¿ÁÓˆÛË Dandy Walker ‹ ·Ú·ÏÏ·Á‹˜ ÙÔ˘, ÌÂٷ͇ 21 ‚‰ÔÌ¿‰ˆÓ Î·È ÙÔ˘ ÙÔÎÂÙÔ‡ . µÚ‹Î·Ó fiÙÈ Ë Û˘¯ÓfiÙËÙ· ÙˆÓ Û˘-ÓÔ‰ÒÓ ˘ÂÚ˯ÔÁÚ·ÊÈο ‰È·ÈÛÙÔ˘Ì¤ÓˆÓ Â˘-ÚËÌ¿ÙˆÓ ‰ÂÓ ‹Ù·Ó ÛÙ·ÙÈÛÙÈο ÛËÌ·ÓÙÈο ˘„Ë-ÏfiÙÂÚË ·Ó¿ÌÂÛ· Û ¤Ì‚Ú˘· Ì Dandy Walker Ô˘ ‰È·ÈÛÙÒıËΠÚÈÓ ÙȘ 21 ‚‰ÔÌ¿‰Â˜ Ù˘ ·ËÛ˘ ÂÓ Û¯¤ÛÂÈ Ì ·˘Ù‹ Ô˘ ‚Ú¤ıËΠ·ÚÁfi-ÙÂÚ· ÂÓ‰ÔÌËÙÚ›ˆ˜.(8 ·fi 14 Î·È 5 ·fi 14) Î·È ÔÈ ¯ÚˆÌÔۈ̷ÙÈΤ˜ ·ÓˆÌ·Ï›Â˜ ‹Ù·Ó ÛËÌ·ÓÙÈ-ο ÈÔ Û˘¯Ó¤˜ ÌÂٷ͇ Â̂ڇˆÓ Ì ÚÒÈÌË ·Ó·ÁÓÒÚÈÛË ÙÔ˘ Û˘Ó‰ÚfiÌÔ˘. ∏ ÎÏÈÓÈ΋ ÛËÌ·Û›· ÙˆÓ ·Ú·ÏÏ·ÁÒÓ ÙÔ˘ Û˘Ó-‰ÚfiÌÔ˘ ¤¯ÂÈ ÂÍÂÙ·ÛÙ› Ù· ÚÔËÁÔ‡ÌÂÓ· ¯Úfi-ÓÈ·. ™Â Ì›· ÌÂϤÙË ·fi ÙÔÓ Chang Î·È Û˘Ó.15 ÂÍÂÙ¿ÛÙËÎ·Ó Ù· ˘ÂÚ˯ÔÁڷʋ̷ٷ 65 ÂÌ-‚Ú‡ˆÓ Ì ·ÁÂÓÂÛ›· ÙÔ˘ ÛÎÒÏËη (37 ηÙÒÙÂ-ÚÔ˘ Ù̷̋ÙÔ˜ ·ÁÂÓÂÛ›·,28 Ì ϋÚË ·ÁÂÓÂÛ›·) ªfiÓÔÓ 22 ·fi Ù· 65 ¤Ì‚Ú˘· ¤˙ËÛ·Ó Ì¤¯ÚÈ ÙÔÓ ÙÔÎÂÙfi Î·È 9 ·fi Ù· 22 ˙ÒÓÙ· ÓÂÔÁÓ¿ η٤-ÏËÍ·Ó Î·Ù¿ ÙÔÓ ÚÒÙÔ ¯ÚfiÓÔ Ù˘ ˙ˆ‹˜ ÙÔ˘˜. ™˘ÓÔ‰¤˜ ·ÓˆÌ·Ï›Â˜ ‚ÚÂı‹Î·Ó Û 75% ÙˆÓ ÓÂÔ-ÁÓÒÓ Ì ϋÚË ·ÁÂÓÂÛ›· ÙÔ˘ ÛÎÒÏËη Î·È Û 76% ÙˆÓ ÓÂÔÁÓÒÓ Ì ˘ÔÏ·Û›· ÙÔ˘ ηÙÒÙÂ-ÚÔ˘ Ù̷̋ÙÔ˜ ÙÔ˘ ÛÎÒÏËη. ∫·Ú˘ÔÙ˘ÈΤ˜
·ÓˆÌ·Ï›Â˜ ‚ÚÂı‹Î·Ó Û 32% ÙˆÓ Â̂ڇˆÓ Ì ϋÚË ·ÁÂÓÂÛ›· ÙÔ˘ ÛÎÒÏËη Î·È 53% Û ¤Ì-‚Ú˘· Ì ·Ï·Û›· ÙÔ˘ ηÙÒÙÂÚÔ˘ Ù̷̋ÙÔ˜. √È ÈÔ Û˘¯Ó¤˜ ¯ÚˆÌÔۈ̷ÙÈΤ˜ ·ÓˆÌ·Ï›Â˜ ‹Ù·Ó ÙÚÈۈ̛· 13, 21 Î·È 18. ∂¯ÂÈ Â›Û˘ ÂÚÈÁÚ·Ê› Ë ÔÈÎÔÁÂÓ‹˜ ·ÁÂÓÂÛ›· ÙÔ˘ ÛÎÒÏËη Ù˘ ·ÚÂÁÎÂÊ·Ï›‰·˜ (™‡Ó‰ÚÔÌÔ Joubert). ∏ ÔÈÎÔÁÂÓ‹˜ ·ÁÂÓÂÛ›· ÙÔ˘ ÛÎÒÏËη Û˘Óԉ‡ÂÙ·È Ì ÂÂÈÛfi‰È· ˘ÂÚηӛ·˜, ·ıÔ-ÏÔÁÈΤ˜ ÎÈÓ‹ÛÂȘ ÙˆÓ ÔÊı·ÏÌÒÓ, ·Ù·Í›·, ÓÔËÙÈ-΋ ηı˘ÛÙ¤ÚËÛË Î·È ÎÏËÚÔÓÔÌÂ›Ù·È Ì ·˘ÙÔ-ۈ̷ÙÈÎfi ˘ÔÏÂÈfiÌÂÓÔ ÙÚfiÔ.16 ™Â Ì›· ÔÈÎÔÁ¤ÓÂÈ· ·˘ÍË̤ÓÔ˘ ÎÈÓ‰‡ÓÔ˘, ÏfiÁˆ ÈÛÙÔÚÈÎÔ‡, ‰È·ÙÂٷ̤ÓË ÌÂÁ¿ÏË ‰ÂÍ·ÌÂÓ‹ ‚Ú¤-ıËΠÛÙȘ 25 ‚‰ÔÌ¿‰Â˜ Ù˘ ·ËÛ˘, ÂÓÒ ÔÏ-ϷϤ˜ ÂÍÂÙ¿ÛÂȘ ÓˆÚ›ÙÂÚ· ÛÙËÓ Î‡ËÛË ‰ÂÓ ‹Ù·Ó ‰È·ÁÓˆÛÙÈΤ˜.17,18 Èڛ˜ ÔÈÎÔÁÂÓ¤˜ ÈÛÙÔÚÈÎfi ÙÔ Û‡Ó‰ÚÔÌÔ Joubert ‰ÂÓ ÌÔÚ› Ó· ‰È·ÎÚÈı› ˘ÂÚ˯ÔÁÚ·-ÊÈο ·fi ÌÂÌÔӈ̤ÓË Dandy Walker ‰È·Ù·Ú·-¯‹. ∏ ÚÔÁÂÓÓËÙÈ΋ ‰È¿ÁÓˆÛË Á›ÓÂÙ·È Ì ÂÈ-ÛÎfiËÛË ÙˆÓ ·ÚÂÁÎÂÊ·ÏȉÈÎÒÓ ËÌÈÛÊ·ÈÚ›ˆÓ Î·È Ù˘ ÌÂÁ¿Ï˘ ‰ÂÍ·ÌÂÓ‹˜, ·ÍÈÔÏÔÁÒÓÙ·˜ ÙË Û˘ÌÌÂÙÚ›· ÙÔ˘˜ Î·È Û˘ÁÎÚ›ÓÔÓÙ·˜ ÙȘ ÌÂÙÚ‹ÛÂȘ ÙÔ˘˜ Ì ηıÔÚÈṲ̂ӷ ÓÔÌÔÁÚ¿ÌÌ·Ù·. ¢È·ÊÔÚÈ΋ ‰È¿ÁÓˆÛË Ú¤ÂÈ Ó· Á›ÓÂÙ·È fiÙ·Ó ·Ó¢ڛÛÎÂÙ·È Ì›· ·ÛÙË ÙÔ˘ ÔÈÛı›Ô˘ ‚fiıÚÔ˘ ·fi ·Ú·¯ÓÔÂȉ‹ ·ÛÙË.19 ª›· ÔÈÛıÔ·ÚÂÁÎÂÊ·ÏȉÈ΋ ·Ú·¯ÓÔÂȉ‹˜ ·ÛÙË Â›Ó·È ÏÈÁfiÙÂÚÔ Û˘¯Ó‹ Î·È ÈÔ ‹È· ·Óˆ-Ì·Ï›· ·fi ÙÔ Û‡Ó‰ÚÔÌÔ Dandy Walker, ‰ÈfiÙÈ ÛÙËÓ ÂÚ›ÙˆÛË ·˘Ù‹ Ô ˘ÔΛÌÂÓÔ˜ ÂÁΤʷ-ÏÔ˜ Â›Ó·È Û¯ËÌ·ÙÈṲ̂ÓÔ˜ Ê˘ÛÈÔÏÔÁÈο. ∞˘Ù‹ Ë ‚Ï¿‚Ë ¿ÓÙ· ‰ËÌÈÔ˘ÚÁ› ¤Ó· ÈÂÛÙÈÎfi Ê·È-ÓfiÌÂÓÔ ·ÏÏ¿ Û ·ÓÙ›ıÂÛË Ì ÙËÓ Î˘ÛÙÈ΋ Ì¿-˙· Ô˘ ‰È·¯ˆÚ›˙ÂÈ Ù· ·ÚÂÁÎÂÊ·ÏȉÈο ËÌÈ-ÛÊ·›ÚÈ· ÛÙÔ Û‡Ó‰ÚÔÌÔ Dandy Walker Ë ·Ú·-¯ÓÔÂȉ‹˜ ·ÛÙË Ù· ÌÂÙ·ÙÔ›˙ÂÈ Û˘ÓÔÏÈο. ªÈ· Ù¤ÙÔÈ· Ì¿˙· ı· ·Ó˘„ÒÛÂÈ Â›Û˘ ÙÔ ÛÎËÓ›‰ÈÔ. ŒÙÛÈ ·˘Ùfi ÙÔ ¯·Ú·ÎÙËÚÈÛÙÈÎfi ‰ÂÓ ÌÔÚ› Ó· Â›Ó·È ‰È·ÊÔÚԉȷÁÓˆÛÙÈÎfi. ∂›Ó·È ÛËÌ·ÓÙÈÎfi ÛÙËÓ ÂÎÙ›ÌËÛË ÂÓfi˜ ÂÌ‚Ú‡Ô˘ Ì ·ÛÙË ÙÔ˘ Ô›ÛıÈÔ˘ ‚fiıÚÔ˘ Ó· ÂÏÂÁ¯ıÔ‡Ó ÚÔÛÂÎÙÈο ÔÈ ‰Ô̤˜ Ù˘ ̤Û˘ ÁÚ·ÌÌ‹˜ ¿ÓˆıÂÓ ÙÔ˘ ÛÎË-Óȉ›Ô˘.20Ÿˆ˜ ¤¯ÂÈ ÛËÌÂȈı› ÓˆÚ›ÙÂÚ·, ÎÔÈ-ÏÈÔÌÂÁ·Ï›· ÌÔÚ› Ó· ·ÚÔ˘ÛÈ·ÛÙ› Î·È Ó· ·ÔÙÂÏ› ·ÏËı‹ ˘‰ÚÔΤʷÏÔ ‹ ÎÔÏÔÎÂÊ·Ï›· Ô˘ Û˘Óԉ‡ÂÙ·È ·fi ·ÁÂÓÂÛ›· ÙÔ˘ ÌÂÛÔÏÔ‚›-Ô˘. ¶Ú¤ÂÈ Ó· ·Ó·˙ËÙËıÔ‡Ó ÛÙÔȯ›· ˘ÂÚË-¯ÔÁÚ·ÊÈο Ù˘ ·ÁÂÓÂÛ›·˜ ÙÔ˘ ÌÂÛÔÏÔ‚›Ô˘. ªÂÁ¿ÏË ÔÈÛıÔ·ÚÂÁÎÂÊ·ÏȉÈ΋ ·Ú·¯ÓÔÂÈ-‰‹˜ ·ÛÙË ÌÔÚ› Ó· ÚÔηϤÛÂÈ ‰È¿Ù·ÛË ÙˆÓ ÎÔÈÏÈÒÓ ·fi Û˘Ì›ÂÛË ·ÏÏ¿ ÔÈ Î‡ÛÙÂȘ ·˘Ù¤˜ ‰ÂÓ Û˘Óԉ‡ÔÓÙ·È Ì ·ÁÂÓÂÛ›· ÙÔ˘ ÌÂÛÔÏfi‚È-Ô˘ ‹ ÎÔÏÔÎÂÊ·Ï›·. ∞ӈ̷ϛ· Arnold – Chiari ∏ ·ÓˆÌ·Ï›· Arnold-Chiari Â›Ó·È ·ÓˆÌ·Ï›· ÙÔ˘ Ô›ÛıÈÔ˘ ÂÁÎÂÊ¿ÏÔ˘ Ô˘ ·ÔÙÂÏÂ›Ù·È ·fi ‰‡Ô ÛΤÏË. ∆Ô ÚÒÙÔ Â›Ó·È ‰È·ÊfiÚÔ˘ ‚·ıÌÔ‡ ÌÂÙ·ÙfiÈÛË ÈÛÙÔ‡ Ô˘ ÚÔ¤Ú¯ÂÙ·È ·fi ÙÔ Î·ÙÒÙÂÚÔ Ù̷̋ ÙÔ˘ ÛÎÒÏËη Ù˘ ·-ÚÂÁÎÂÊ·Ï›‰·˜ ̤۷ ÛÙÔ ·ÓÒÙÂÚÔ ÛÔÓ‰˘ÏÈÎfi ÙÚ‹Ì·. ∆Ô ‰Â‡ÙÂÚÔ Â›Ó·È Ì›· fiÌÔÈ· Ô˘Ú·›· ÌÂÙ·ÙfiÈÛË Ù˘ Á¤Ê˘Ú·˜, Ù˘ ٤ٷÚÙ˘ ÎÔÈ-Ï›·˜ Î·È ÙÔ˘ ÚÔÌ‹ÎË Ì˘ÂÏÔ‡ ‰È·Ì¤ÛÔ˘ ÙÔ˘ ÌÂÁ¿ÏÔ˘ ÙÚ‹Ì·ÙÔ˜ ̤۷ ÛÙÔ ÛÔÓ‰˘ÏÈÎfi ·˘-Ïfi. ∞˘Ùfi Û˘Ó‹ıˆ˜ Û˘Óԉ‡ÂÙ·È Ì ˘‰ÚÔΤʷ-ÏÔ Î·È ÌËÓÓÈÁÁÔÌ˘Â˘‰ÚÔΤʷ-ÏÔ΋ÏË.21 ∞ӷʤÚÂÙ·È fiÙÈ ÔÈ ÂÚÈÛÛfiÙÂÚ˜ ÂÚÈÙÒÛÂȘ ‰Èۯȉԇ˜ Ú¿-¯Ë˜ ÂÈϤÎÔÓÙ·È ·fi ÙËÓ ‰È·Ù·Ú·¯‹ Arnold Chiari Î·È fiÙÈ 90 ¤ˆ˜ 95% ·˘ÙÒÓ ÙˆÓ ·ÛıÂ-ÓÒÓ ·ÚÔ˘ÛÈ¿˙Ô˘Ó ˘‰ÚÔΤʷÏÔ.22,23 ∏ ‰È·Ù·-Ú·¯‹ Arnold Chiari ·ÔÙÂÏ› ¤Ó·Ó ÛËÌ·ÓÙÈÎfi ‰Â›ÎÙË ÁÈ· ÙË ‰Èۯȉ‹ Ú¿¯Ë. ¢‡Ô ·ıÔÁÓˆÌÈ-ο ˘ÂÚ˯ÔÁÚ·ÊÈ·ıÔÁÓˆÌÈ-ο ÛËÌ›· ¤¯Ô˘Ó ÂÚÈÁÚ·-Ê› ÁÈ· ÙË ‰È·Ù·Ú·¯‹ Arnold Chiari Î·È Â›Ó·È ÙÔ ÛËÌÂ›Ô ÙÔ˘ ÏÂÌÔÓÈÔ‡ fiÔ˘ ÂÌ‚¿ı˘ÓÛË ÙˆÓ ÌÂوȷ›ˆÓ ÔÛÙÒÓ ÌÔÚ› Ó· ‰ÒÛÂÈ Ì›· Û¯‹-Ì·ÙÔ˜ ÏÂÌÔÓÈÔ‡ ‰È·ÌfiÚʈÛË ÛÙÔ ÎÚ·Ó›Ô ÙÔ˘ ÚÔۂ‚ÏË̤ÓÔ˘ ÂÌ‚Ú‡Ô˘ Û ÂÁοÚÛÈ· ÙÔÌ‹ ÛÙË ‰È¿ÚÎÂÈ· ÙÔ˘ ‰Â˘Ù¤ÚÔ˘ ÙÚÈÌ‹ÓÔ˘. ∏ Ô˘-Ú·›· ÌÂÙ·ÙfiÈÛË ÙÔ˘ ÂÁÎÂÊ·ÏÈÎÔ‡ ÈÛÙÔ‡ Ê·›-ÓÂÙ·È Ó· ·Ú¿ÁÂÈ ·˘Ù‹ ÙËÓ ÂÌ‚¿ı˘ÓÛË. ∏ ÌÂ-Ù·ÙfiÈÛË Ù˘ ·ÚÂÁÎÂÊ·Ï›‰Ô˜ ·Ú·ÌÔÚÊÒ-ÓÂÈ Ù· ËÌÈÛÊ·›ÚÈ· Ù˘ (Ù· ÔÔ›· ¯¿ÓÔ˘Ó ÙÔ ÛÊ·ÈÚÈÎfi ÙÔ˘˜ Û¯‹Ì·) Á›ÓÔÓÙ·È Â›Â‰·, Ë ÌÂ-Á¿ÏË ‰ÂÍ·ÌÂÓ‹ Û˘ÌȤ˙ÂÙ·È Î·È ÙÔ ÂÓÙ‡ˆÌ· ÙÔ˘ ÛÎÒÏËη Ê·›ÓÂÙ·È ÂÚÈÛÛfiÙÂÚÔ Û˘Ó¯¤˜ Î·È ÚÔ·ÙÂÈ ÙÔ ÛËÌÂ›Ô Ù˘ Ì·Ó¿Ó·˜, ÙÔ ÔÔ›Ô ÌÔÚ› Ó· Ê·Ó› ·fi ÙÔ ÚÒÙÔ ÙÚ›ÌË-ÓÔ.24 ™Â ·ÎÚ·›Â˜ ÂÚÈÙÒÛÂȘ Ù· ·ÚÂÁÎÂÊ·-ÏȉÈο ËÌÈÛÊ·›ÚÈ· ÌÔÚ› Ó· ÌËÓ ÂÌÊ·Ó›˙Ô-ÓÙ·È Î·Ù¿ ÙË ‰È¿ÚÎÂÈ· ÙÔ˘ ˘ÂÚ˯ÔÁÚ·ÊÈÎÔ‡ ÂϤÁ¯Ô˘ Ù˘ ÎÂÊ·Ï‹˜ ÙÔ˘ ÂÌ‚Ú‡Ô˘. ∞˘Ù‹ Ë ¯·Ú·ÎÙËÚÈÛÙÈ΋ ˘ÂÚ˯ÔÁÚ·ÊÈ΋ ÂÌÊ¿ÓÈÛË
Ú¤ÂÈ Ó· ÎÈÓËÙÔÔÈ‹ÛÂÈ ÙÔÓ ˘ÂÚ˯ÔÁÚ·ÊÈ-ÛÙ‹ ÁÈ· Ó· „¿ÍÂÈ ÁÈ· ‰Èۯȉ‹ Ú¿¯Ë.25-28
Posterior fossa abnormalities –
Dandy Walker Syndrome
Ch. ∫allideri, D. ∫assanos, ∂. ™alamalekis
3rd Department of Obstetrics and Gynaecology, University of Athens P.G.N. ”Attikon”, Athens, Greece AÏÏËÏÔÁÚ·Ê›·: D. Kassanos
1 Rimini str., 12462 Chaidari, Greece ∆el.: 210-5831000, direct: 2214 E-mail: [email protected]
Summary
Dandy Walker syndrome indicates the associ-ation of 1) ventriculomegaly of variable de-gree 2) a large cisterna magna 3) a defect in the cerebellar vermis through which the cyst communicates with the fourth ventricle. A wide spectrum of anomalies of the posterior fossa have been described but there are no clear criteria of distinction between them 1) classic Dandy Walker malformation, (en-larged posterior fossa, complete or partial agenesis of the cerebellar vermis and elevated tentorium) 2) the Dandy Walker variant (vari-able hypoplasia of the cerebellar vermis with or without enlargement of the posterior fossa) and 3) megacisterna magna (enlarged cisterna magna with integrity of both cerebellar vermis and fourth ventricle). Familial agenesis of the cerebellar vermis with episodic hypercapnia, abnormal eye movements , ataxia and early death define Jouberts syndrome. Without a family history of Jouberts syndrome, familial agenesis of cerebellar vermis would not be distinguishable sonographically from an iso-lated Dandy Walker malformation.
The Arnold Chiari malformation is an anom-aly of the hindbrain, with two components. The first a variable displacement of tissue
de-rived from the inferior cerebellar vermis into the upper cervical canal. The second a similar caudal dislocation of the pons, the fourth ven-tricleand mededulla oblonganda to the spinal canal. Usually is associated with hydro-cephalus and spina bifida.
Key words: Dandy Walker syndrome, abnormalities of the
ver-mis, enlargement of the fourth ventricle
µÈ‚ÏÈÔÁÚ·Ê›·
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