別紙４

(1)

11 別紙４

研究成果の刊行に関する一覧表（平成28年度～平成30年度）

書籍

著者氏名論文タイトル名書籍全体の

編集者名書籍名出版社名出版地出版年ページなし

雑誌平成28年度

発表者氏名論文タイトル名発表誌名巻号ページ出版年

田村雄一レジストリー比較からみた日本

における肺高血圧症の治療

呼吸と循

環 64(6) 548-553 2016

Ogawa A, Satoh T, Tamura Y, Fukuda K, Matsubara H

Survival of Japanese Patients With Idiopathic/Heritable Pulmonary Arterial Hypertension.

Am J Cardiol.

119(9) 1479-1484 2017

平成29年度

Tamura Y, Kumamaru H, Satoh T, Miyata H, Ogawa A, Tanabe N, Hatano M, Yao A, Abe K, Tsujino I, Fukuda K, Kimura H, Kuwana M, Matsubara H, Tatsumi K; Japan PH Registry (JAPHR) Network

Effectiveness and Outcome of Pulmonary Arterial

Hypertension-Specific Therapy in Japanese Patients With Pulmonary Arterial Hypertension.

Circ J. 82 275-282 2018

田村雄一、古川明日香、

倉石博、巽浩一郎, Jenelle Yorke

肺高血圧症疾患特異的PRO指標 emPHasis-10日本語版の開発と言語的妥当性

日呼吸誌 7(2) 79-84 2018

Kimura G, Kataoka M, Inami T, Fukuda K, Yoshino H, Satoh T

Sorafenib as a potential strategy for refractory pulmonary arterial hypertension.

Pulm Pharmacol Ther

44 46-49 2017

Satoh T Diagnosis and Treatment of Pulmonary Hypertension Editor Yoshihiro Fukumoto. Medical Therapy for Chronic

Thromboembolic Pulmonary Hypertension.

Springer 185-192 2017

Ogawa A, Satoh T, Fukuda T, Sugimura K, Fukumoto Y, Emoto N, Yamada N, Yao A, Ando M, Ogino H, Tanabe N, Tsujino I, Hanaoka M, Minatoya K, Ito H, Matsubara H

Balloon Pulmonary Angioplasty for Chronic Thromboembolism.

Circ Cardiovasc Qual Outcomes

10 e004029 2017

Gamou S, Kataoka M, Aimi Y, Chiba T, Momose Y, Isobe S, Hirayama T, Yoshino H, Fukuda K, Satoh T

Genetics in pulmonary arterial hypertension in a large

homogeneous Japanese population.

Clin Genet. 94(1) 70-80 2018

(2)

12 Jujo-Sanada T, Tanabe N,

Sakao S, Sugiura T, Sekine A, Nishimura R, Suda R, Naito A, Miwa H, Yamamoto K, Sasaki A, Matsumura A, Ema R, Kasai H, Kato F, Tatsumi K

The anticoagulant effects of warfarin and the bleeding risk associated with its use in patients with chronic thromboembolic pulmonary hypertension at a specialist center in Japan: a retrospective cohort study.

Pulm Circ. 7 684-691 2017

Suda R, Tanabe N, Ishida K, Kato F, Urushibara T, Sekine A, Nishimura R, Jujo T, Sugiura T, Shigeta A, Sakao S, Tatsumi K

Prognostic and pathophysiological marker for patients with chronic thromboembolic pulmonary hypertension: Usefulness of diffusing capacity for carbon monoxide at diagnosis.

Respirolog y.

22 179-186 2017

Kato F, Sakao S, Takeuchi T, Suzuki T, Nishimura R, Yasuda T, Tanabe N, Tatsumi K

Endothelial cell-related autophagic pathways in

Sugen/hypoxia-exposed pulmonary arterial hypertensive rats.

Am J Physiol Lung Cell Mol Physiol.

313 L899-L915 2017

Kasai H, Tanabe N,

Fujimoto K, Hoshi H, Naito J, Suzuki R, Matsumura A, Sugiura T, Sakao S, Tatsumi K

Mosaic attenuation pattern in non-contrast computed

tomography for the assessment of pulmonary perfusion in chronic thromboembolic pulmonary hypertension.

Respir Investig.

55 300-307 2017

Ema R, Sugiura T, Kawata N, Tanabe N, Kasai H, Nishimura R, Jujo T, Shigeta A, Sakao S, Tatsumi K

The dilatation of main pulmonary artery and right ventricle observed by enhanced chest computed tomography predict poor outcome in inoperable chronic

thromboembolic pulmonary hypertension.

Eur J Radiol.

94 70-77 2017

Abe M, Tsushima K, Ikari J, Kawata N, Terada J, Tanabe N, Tatsumi K

Evaluation of the clinical characteristics of

everolimus-induced lung injury and determination of associated risk factors.

Resp Med. 134 6-11 2017

Yamamoto K, Tanabe N, Suda R, Sasaki A, Matsumura A, Ema R, Kasai H, Kato F, Sekine A, Nishimura R, Jujo T, Sugiura T, Shigeta A, Sakao S, Tatsumi K

Riociguat for patients with chronic thromboembolic pulmonary hypertension: usefulness of transitioning from

phosphodiesterase type 5 inhibitor.

Respir Investig.

55 270-275 2017

Inagaki T, Terada J, Yahaba M, Kawata N, Jujo T, Nagashima K, Sakao S, Tanabe N, Tatsumi K

Heart rate and oxygen saturation change patterns during a 6-min walk test in subjects with chronic thromboembolic pulmonary hypertension.

Respir Care

63（5） 573-583 2018

Ozawa K, Funabashi N, Takaoka H, Tanabe N, Tatsumi K, Kobayashi Y

Detection of right ventricular myocardial fibrosis using

quantitative CT attenuation of the right ventricular myocardium in the late phase on 320 slice CT in subjects with pulmonary

hypertension.

Int J Cardiol.

228 165-168 2017

(3)

13 Tamura Y, Kumamaru H,

Satoh T, Miyata H, Ogawa A, Tanabe N, Hatano M, Yao A, Abe K, Tsujino I, Fukuda K, Kimura H, Kuwana M, Matsubara H, Tatsumi K on behalf of the Japan PH Registry (JAPHR) Network.

Effectiveness and outcome of pulmonary arterial

hypertension-specific therapy in Japanese patients with pulmonary arterial hypertension.

Circ J. 82(1) 275-282 2017

Kimura M, Tamura Y, Guignabert C, Takei M, Kosaki K, Tanabe N, Tatsumi K, Saji T, Satoh T, Kataoka M, Kamitsuji S, Kamatani N, Thuillet R, Tu L, Humbert M, Fukuda K, Sano M

A genome-wide association analysis identifies

PDE1A|DNAJC10 locus on chromosome 2 associated with idiopathic pulmonary arterial hypertension in a Japanese population.

Oncotarget .

8 74917-749 26

2017

Nakamura H, Kato M, Nogochi A, Ohira H, Tsujino I, Atsumi T

Efficient detection of pulmonary arterial hypertension using serum haptoglobin level and cardiac MRI in patients with connective tissue diseases: a pilot study.

Clin Exp Rheumatol

36(2) 345-346 2018

Shoji T, Mizugaki H, Ikezawa Y, Furuta M, Takashima Y, Kikuchi H, Goudarzi H, Asahina H, Kikuchi J, Kikuchi E, Sakakibara-Konishi J, Shinagawa N, Tsujino I, Nishimura M

Successful Application of Edoxaban in the Treatment of Venous Thromboembolism Recurrence in a Patient with Non-small Cell Lung Cancer after Tumor Shrinkage.

Intern Med.

57(12) 1769-1772 2018

Sato T, Tsujino I, Ohira H, Oyama-Manabe N, Ito YM, Takashina C, Watanabe T, Nishimura M

Accuracy of echocardiographic indices for serial monitoring of right ventricular systolic function in patients with precapillary pulmonary hypertension.

PLoS One 12(11) e0187806 2017

Shimizu K, Tsujino I, Sato T, Sugimoto A, Nakaya T, Watanabe T, Ohira H, Ito YM, Nishimura M

Performance of computed tomography-derived pulmonary vasculature metrics in the diagnosis and haemodynamic assessment of pulmonary arterial hypertension.

Eur J Radiol

96 31-36 2017

Balloon Pulmonary Angioplasty for Chronic Thromboembolic Pulmonary Hypertension: Results of a Multicenter Registry.

Circ Cardiovasc Qual Outcomes

10(11) e004029 2017

Nakamura H, Kato M, Nakaya T, Kono M,

Tanimura S, Sato T, Fujieda Y, Oku K, Ohira H,

Bohgaki T, Yasuda S, Tsujino I, Nishimura M, Atsumi T

Decreased haptoglobin levels inversely correlated with pulmonary artery pressure in patients with pulmonary arterial hypertension: A cross-sectional study

Medicine (Baltimore )

96(43) e8349 2017

Sato T, Ohira H, Tsujino I Representative Chest Auscultation Findings in Pulmonary

Hypertension: Phonocardiograms and Sound Clips.

Ann Am Thorac Soc

14(5) e1-3 2017

(4)

14 Tanabe N, Ikeda S, Tahara

N, Fukuda K, Hatano M, Ito H, Nakayama T, Anzai T, Hashimoto A, Inoue T, Kajinami K, Kihara Y, Kinoshita H, Kuwahara K, Murohara T, Okazaki O, Sakai S, Satoh T, Takeda Y, Takeishi Y, Taniguchi M, Watanabe H, Yamamoto T, Yamauchi-Takihara K, Yoshioka K, Sasayama S

Efficacy and Safety of an Orally Administered Selective

Prostacyclin Receptor Agonist, Selexipag, in Japanese Patients With Pulmonary Arterial Hypertension.

Circ J. 81(9) 1360-1367 2017

Shirai Y, Kuwana M Complex pathophysiology of pulmonary hypertension associated with systemic sclerosis: potential unfavorable effects of pulmonary vasodilators.

J.

Scleroderm a Relat.

Disord

2(2) 92-99 2017

Coghlan JG, Galiè N, Barberà JA, Frost AE, Ghofrani HA, Hoeper MM, Kuwana M, McLaughlin VV, Peacock AJ,

Simonneau G, Vachiéry JL, Blair C, Gillies H, Miller KL, Harris JHN, Langley J, and Rubin LJ

Initial combination therapy with ambrisentan and tadalafil in connective tissue

disease-associated pulmonary arterial hypertension (CTD-PAH):

subgroup analysis from the AMBITION trial.

Ann.

Rheum

76(7) 1219-1227 2017

Yasuoka Y, Shirai Y, Tamura Y, Takeuchi T, Kuwana M

Predictors for favorable responses to immunosuppressive treatment in pulmonary arterial hypertension associated with connective tissue disease

Circ. J 82(1) 546-554 2018

Mihara K, Ogawa A, Matsubara H, Terao T, Ichikawa Y

Investigation of safety and efficacy of the new more thermostable formulation of Flolan

(epoprostenol) in Japanese patients with pulmonary arterial

hypertension (PAH)-An open-label, single-arm study.

PLoS One. 13 e0195195 2018

Ogawa A, Satoh T, Tamura Y, Fukuda K, Matsubara H

Survival of Japanese Patients With Idiopathic/Heritable Pulmonary Arterial Hypertension.

Am J Cardiol.

119 1479-1484 2017

Balloon Pulmonary Angioplasty for Chronic Thromboembolic Pulmonary Hypertension: Results of a Multicenter Registry.

Circ Cardiovasc Qual Outcomes.

10 e004029 2017

Ogawa A, Miyaji K, Matsubara H

Efficacy and safety of long-term imatinib therapy for patients with pulmonary veno-occlusive disease and pulmonary capillary

hemangiomatosis.

Respir Med.

131 215-219 2017

Ogawa A, Takahashi Y, Matsubara H.

Clinical prediction score for identifying patients with pulmonary veno-occlusive disease/pulmonary capillary hemangiomatosis.

J Cardiol. 72(3) 255-260 2018

(5)

15 Hosokawa K, Abe K,

Horimoto K, Yamasaki Y, Nagao M, Tsutsui H

Balloon Pulmonary Angioplasty Relieves Hemodynamic Stress towards Untreated-Side Pulmonary Vasculature and Ameliorates Its Resistance in Patients with Chronic Thromboembolic Pulmonary Hypertension.

EuroInterv ention

20 2069-2076 2018

Hosokawa K, Yamamoto T, Abe K, Tsutsui H

Delayed-onset Lung Injury After Balloon Pulmonary Angioplasty.

Eur Heart J Cardiovasc Imaging.

18 275-282 2017

Tanaka M, Abe K, Oka M, Saku K, Yoshida K, Ishikawa T, McMurtry IF, Sunagawa K, Hoka S, Tsutsui H

Inhibition of Nitric Oxide Synthase Unmasks Vigorous

Vasoconstriction in Established Pulmonary Arterial Hypertension.

Physiol Rep.

82 1426 2017

Hosokawa K, Abe K, Kashihara S, Tsutsui H

Three Dimensional SPECT/CT Fusion Imaging Guided Balloon Pulmonary Angioplasty for Chronic Thromboembolic Pulmonary Hypertension.

JACC Cardiovasc Interv.

10 e193-194 2017

平成30年度

Galiè N, Channick RN, Frantz RP, Grünig E, Jing ZC, Moiseeva O, Preston IR, Pulido T, Safdar Z, Tamura Y, McLaughlin VV

Risk stratification and medical therapy of pulmonary arterial hypertension.

Eur Respir J.

53(1) pii:

1801889

2018

Tanabe N, Kawakami T, Satoh T, Matsubara H, Nakanishi N, Ogino H, Tamura Y, Tsujino I, Ogawa A, Sakao S, Nishizaki M, Ishida K, Ichimura Y, Yoshida M, Tatsumi K

Balloon pulmonaty angioplasty for chronic thromboembolic

pulmonary hypertension: A systematic review.

Respir Investig.

56(4) 332-341 2018

Tamura Y, Phan C, Tu L, Le Hiress M, Thuillet R, Jutant EM, Fadel E, Savale L, Huertas A, Humbert M, Guignabert C

Ectopic upregulation of membrane-bound IL6R drives vascular remodeling in pulmonary arterial hypertension.

J Clin Invest.

128(5) 1956-1970 2018

Kawasaki T, Chen W, Htwe YM, Tatsumi K, Dudek SM

DPP4 inhibition by sitagliptin attenuates LPS-induced lung injury in mice.

315 L834-845 2018

Abe M, Tsushima K, Sakayori M, Suzuki K, Ikari J, Terada J, Tatsumi K

Utility of nintedanib for severe idiopathic pulmonary fibrosis: a single-center retrospective study.

Drug Des Devel Ther.

12 3369-3375 2018

Abe M, Tsushima K, Ikari J, Kawata N, Terada J, Tanabe N, Tatsumi K

Evaluation of the clinical characteristics of

everolimus-induced lung injury and determination of associated risk factors.

Respir Med.

134 6-11 2018

Matsumura T, Tsushima K, Abe M, Suzuki K,

Yamagishi K, Matsumura A, Ichimura Y, Ikari J, Terada J, Tatsumi K

The effects of pirfenidone in patients with an acute exacerbation of interstitial pneumonia.

Clin Respir J.

12 1550-1558 2018

(6)

16 Matsumura T, Terada J,

Kinoshita T, Sakurai Y, Yahaba M, Tsushima K, Sakao S, Nagashima K, Ozaki T, Nagase H, Kobayashi Y, Hiwasa T, Tatsumi K

Circulating autoantibodies against neuroblastoma suppressor of tumorigenicity 1 (NBL1): a potential biomarker for coronary artery disease in patients with obstructive sleep apnea.

PLoS One 13 e0195015 2018

Naito A, Sakao S, Lang IM, Voelkel NF, Jujo T, Ishida K, Sugiura T, Matsumiya G, Yoshino I, Tanabe N, Tatsumi K

Endothelial cells from pulmonary endarterectomy specimens possess a high angiogenic potential and express high levels of hepatocyte growth factor.

BMC Pulm Med

18 197 2018

Ishiwata T, Abe M, Kasai H, Ikari J, Kawata N, Terada J, Sakao S, Tada Y, Tanabe N, Tatsumi K

Safety of diagnostic flexible bronchoscopy in patients with echocardiographic evidence of pulmonary hypertension.

Respir Investig.

57 73-78 2019

Miwa H, Tanabe N, Jujo T, Kato F, Anazawa R, Yamamoto K, Naito A, Kasai H, Nishimura R, Suda R, Sugiura T, Sakao S, Ishida K, Masuda M, Tatsumi K

Long-term outcome of chronic thromboembolic pulmonary hypertension at a single Japanese pulmonary endarterectomy center.

Circ J. 82 1428-1436 2018

Kinoshita T, Yahaba M, Terada J, Matsumura T, Sakurai Y, Nagashima K, Sakao S, Tatsumi K

Impact of arterial stiffness on WatchPAT variables in patients with obstructive sleep apnea.

J Clin Sleep Med.

14 319-325 2018

Katsumata Y, Terada J, Abe M, Suzuki K, Ishiwata T, Ikari J, Takeda Y, Sakaida E, Tsushima K, Tatsumi K

An analysis of the clinical benefit of 37 bronchoalveolar lavage procedures in patients with hematologic disease and pulmonary complications.

Intern Med.

58(8) 1073-1080 2019

Fujimoto K, Ishiwata T, Kasai H, Terada J, Shionoya Y, Ikari J, Kawata N, Tada Y, Tsushima K, Tatsumi K

Identification of factors during bronchoscopy that affect patient reluctance to undergo repeat examination: Questionnaire analysis after initial bronchoscopy.

PLoS One 13 e0208495 2018

Inagaki T, Terada J, Yahaba M, Kawata N, Jujo T, Nagashima K, Sakao S, Tanabe N, Tatsumi K

Heart rate and oxygen saturation change patterns during 6-min walk test in subjects with chronic thromboembolic pulmonary hypertension.

Respir Care

63 573-583 2018

Haga T, Ito K, Sakashita K, Iguchi M, Ono M, Tatsumi K

Risk factors for pneumonia in patients with schizophrenia.

Neuropsyc hopharmac ol Rep.

38 204-209 2018

Haga T, Ito K, Ono M, Maruyama J, Iguchi M, Suzuki H, Hayashi E, Sakashita K, Nagao T, Ikemoto S, Okaniwa A, Kitami M, Inuo E, Tatsumi K

Risk factors for death due to psychiatric hospital-acquired pneumonia.

Intern Med 57 2473-2478 2018

Suzuki T, Carrier EJ, Talati MH, Rathinasabapathy A, Chen X, Nishimura R, Tada Y, Tatsumi K, West J

Isolation and characterization endothelial-to-mesenchymal transition-cells in pulmonary arterial hypertension.

314 L118-L126 2018

(7)

17 Ogasawara T, Kohashi Y,

Ikari J, Taniguchi T, Tsuruoka N,

Watanabe-Takano H, Fujimura L, Sakamoto A, Hatano M, Hirata H, Fukushima Y, Fukuda T, Kurasawa K, Tatsumi K, Tokuhisa T, Arima M

Allergic TH2 response governed by B-cell lymphoma 6 function in naturally occurring memory phenotype CD4⁺T cells.

Front Immunol.

9 750 2018

Chai K, Ning X, Nguyễn TTT, Zhong B, Morinaga T, Li Z, Shingyoji M, Tada Y, Tatsumi K, Shimada H, Hiroshima K, Yamaguchi N, Tagawa M

Heat shock protein 90 inhibitors augment endogenous wild-type p53 expression but down-regulate the adenovirally-induced

expression by inhibiting a proteasome activity.

Oncotarget 9 26130-261 43

2018

Ishiwata T, Abe M, Kasai H, Ikari J, Kawata N, Terada J, Sakao S, Tada Y, Tanabe N, Tatsumi K.

Safety of diagnostic flexible bronchoscopy in patients with echocardiographic evidence of pulmonary hypertension.

Respir Investig.

57 73-78 2019

Tanaka N, Jujo T, Sugiura T, Matsuura K, Kobayashi T, Naito A, Shimazu K, Kasai H, Suda R,

Nishimura R, Ikari J, Sakao S, Tanabe N, Matsumiya G, Tatsumi K

Partial anomalous pulmonary venous return with dual drainage to the superior vena cava and left atrium with pulmonary

hypertension.

Respir Med Case Rep.

25 112-115 2018

Uehara Y, Kasai H, Nakajima T, Tanabe N, Tatsumi K, Yoshino I

Aspergillus sternomyelitis developed from chronic

pulmonary aspergillosis as a late complication to lobectomy for lung cancer.

Intern Med 57 2991-2994 2018

Shionoya Y, Kasai H, Terada J, Abe M, Takeda Y, Sakaida E, Tanabe N, Tatsumi K

Cytomegalovirus pneumonia with progressive lung volume loss.

Am J Case Rep.

19 1393-1397 2018

Ogawa A, Sakao S, Tanabe N, Matsubara H, Tatsumi K

Use of vasodilators for the treatment of pulmonary veno-occlusive disease and pulmonary capillary

hemangiomatosis: A systematic review.

Respir Investig.

57(2) 183-190 2019

Shimomura I, Abe M, Li Y, Tsushima K, Sakao S, Tanabe N, Ikusaka M, Tatsumi K

Pulmonary hypertension exacerbated by nintedanib administration for idiopathic pulmonary fibrosis.

Intern Med 58 965-968 2019

Naito A, Hiwasa T, Tanabe N, Sanada TJ, Sugiura T, Shigeta A, Terada J, Takizawa H, Kashiwado K, Sakao S, Tatsumi K

Elevated levels of autoantibodies against EXD2 and PHAX in the sera of patients with chronic thromboembolic pulmonary hypertension.

PLoS One 14 e0211377 2019

Ikubo Y, Kasai H, Sugiura T, Saito T, Shoji H, Sakao S, Kasahara Y, Tanabe N, Tatsumi K

Pulmonary hypertension that developed during treatment for hepatopulmonary syndrome and pulmonary arteriovenous malformation.

Intern Med Epub ahead of print

2019

(8)

18 Tanimura S, Kato M, Abe

N, Ohira H, Tsujino I, Atsumi T.

Successful treatment of

tocilizumab-resistant large vessel pulmonary arteritis with

infliximab.

Immunol Med.

41(1) 39-42 2018

Fukuda K, Date H, Doi S, Fukumoto Y, Fukushima N, Hatano M, Ito H, Kuwana M, Matsubara H, Momomura SI, Nishimura M, Ogino H, Satoh T, Shimokawa H,

Yamauchi-Takihara K, Tatsumi K, Ishibashi-Ueda H, Yamada N, Yoshida S, Abe K, Ogawa A, Ogo T, Kasai T, Kataoka M, Kawakami T, Kogaki S, Nakamura M, Nakayama T, Nishizaki M, Sugimura K, Tanabe N, Tsujino I, Yao A, Akasaka T, Ando M, Kimura T, Kuriyama T, Nakanishi N, Nakanishi T, Tsutsui H

Japanese Circulation Society and the Japanese Pulmonary

Circulation and Pulmonary Hypertension Society Joint Working Group. Guidelines for the Treatment of Pulmonary Hypertension (JCS 2017/JPCPHS 2017)

Circ J. 83(4) 842-945 2019

Sato K, Ohira H,

Horinouchi T, Nakaya T, Mazaki Y, Sugimoto A, Watanabe T, Tsujino I, Nishimura M

Chinese herbal medicine Qing-Dai-induced pulmonary arterial hypertension in a patient with ulcerative colitis: A case report and experimental investigation.

Respir Me d Case Re p.

26 265-269 2019

Nakaya T, Tsujino I, Ohira H, Sato T, Watanabe T, Oyama-Manabe N, Nishimura M

Amelioration of right ventricular systolic function and stiffness in a patient with idiopathic pulmonary arterial hypertension treated with oral triple combination therapy.

Pulm Circ. 8(2) 204589401 8765350

2018

Nakamura H, Kato M, Nogochi A, Ohira H, Tsujino I, Atsumi T

Efficient detection of pulmonary arterial hypertension using serum haptoglobin level and cardiac MRI in patients with connective tissue diseases: a pilot study.

Clin Exp Rheumatol .

36(2) 345-346 2018

Shoji T, Mizugaki H, Ikezawa Y, Furuta M, Takashima Y, Kikuchi H, Goudarzi H, Asahina H, Kikuchi J, Kikuchi E, Sakakibara-Konishi J, Shinagawa N, Tsujino I, Nishimura M

Successful Application of Edoxaban in the Treatment of Venous Thromboembolism Recurrence in a Patient with Non-small Cell Lung Cancer after Tumor Shrinkage.

Intern Me d.

57(12) 1769-1772 2018

Watanabe H Treatment Selection in Pulmonary Arterial Hypertension:

Phosphodiesterase Type 5 Inhibitors versus Soluble Guanylate Cyclase Stimulator.

Eur Cardiol

13(1) 35-37 2018

Yasuoka H, Shirai Y, Tamura Y, Takeuchi T, Kuwana M

Predictors of Favorable Responses to Immunosuppressive Treatment in Pulmonary Arterial

Hypertension Associated With Connective Tissue Disease.

Circ J. 82(2) 546-554 2018

(9)

19 Asano Y, Jinnin M,

Kawaguchi Y, Kuwana M, Goto D, Sato S, Takehara K, Hatano M, Fujimoto M, Mugii N, Ihn H

Diagnostic criteria, severity classification and guidelines of systemic sclerosis.

J

Dermatol.

45(6) 633-691 2018

Yasuoka H, Tam YY, Okazaki Y, Tamura Y, Matsuo K,

Feghali-Bostwick C, Takeuchi T, Kuwana M

Fra-1 transgenic mouse as a model for systemic sclerosis: a potential role of M2 polarization.

J

Scleroderm a Relat Disord.

Epub ahead of print Ahn CM, Matsubara H Chronic Thromboembolic

Pulmonary Hypertension:

Endovascular Treatment.

Korean Ci

rc J. 49(3) 214-222 2019 Kim NH, Delcroix M, Jais

X, Madani MM, Matsubara H, Mayer E, Ogo T, Tapson VF, Ghofrani HA, Jenkins DP

Chronic thromboembolic pulmonary hypertension.

Eur Respir

J. 53(1) pii: 18019

15 2019

Ejiri K, Ogawa A, Fujii S, Ito H, Matsubara H

Vascular Injury Is a Major Cause of Lung Injury After Balloon Pulmonary Angioplasty in Patients With Chronic Thromboembolic Pulmonary Hypertension.

Circ Cardi ovasc Inte rv.

11(12) e005884. 2018

Klok FA, Barco S, Konstantinides SV, Dartevelle P, Fadel E, Jenkins D, Kim NH, Madani M, Matsubara H, Mayer E, Pepke-Zaba J, Delcroix M, Lang IM

Determinants of diagnostic delay in chronic thromboembolic pulmonary hypertension: results from the European CTEPH Registry.

Eur Respir

J. 52(6) pii: 18016

87 2018

Nakamura K, Sakaguchi M, Matsubara H, Akagi S, Sarashina T, Ejiri K, Akazawa K, Kondo M, Nakagawa K, Yoshida M, Miyoshi T, Ogo T, Oto T, Toyooka S, Higashimoto Y, Fukami K, Ito H

Crucial role of RAGE in

inappropriate increase of smooth muscle cells from patients with pulmonary arterial hypertension.

PLoS One. 13(9) e0203046. 2018

Akagi S, Matsubara H, Nakamura K, Ito H

Modern treatment to reduce pulmonary arterial pressure in pulmonary arterial hypertension.

J Cardiol. 72(6) 466-472 2018

Sato S, Ogawa A, Matsubara H

Change in R wave in lead V1 predicts survival of patients with pulmonary arterial hypertension.

Pulm Circ. 8(2) 204589401 8776496. 2018 Ogawa A, Matsubara H After the Dawn - Balloon

Pulmonary Angioplasty for Patients With Chronic Thromboembolic Pulmonary Hypertension.

Circ J. 82(5) 1222-1230 2018

Shimokawahara H, Ogawa A, Mizoguchi H, Yagi H, Ikemiyagi H, Matsubara H

Vessel Stretching Is a Cause of Lumen Enlargement Immediately After Balloon Pulmonary

Angioplasty: Intravascular Ultrasound Analysis in Patients With Chronic Thromboembolic Pulmonary Hypertension.

Circ Cardiovasc Interv.

11(4) e006010. 2018

(10)

20 Mihara K, Ogawa A,

Matsubara H, Terao T, Ichikawa Y

Investigation of safety and efficacy of the new more thermostable formulation of Flolan

(epoprostenol) in Japanese patients with pulmonary arterial

hypertension (PAH)-An open-label, single-arm study.

PLoS One. 13(4) e0195195 2018

Ogawa A, Takahashi Y, Matsubara H

Clinical prediction score for identifying patients with pulmonary veno-occlusive disease/pulmonary capillary hemangiomatosis.

J Cardiol. 72(3) 255-260 2018

Hosokawa K, Abe K, Horimoto K, Yamasaki Y, Nagao M, Tsutsui H

Balloon Pulmonary Angioplasty Relieves Hemodynamic Stress towards Untreated-Side Pulmonary Vasculature and Ameliorates Its Resistance in Patients with Chronic Thromboembolic Pulmonary Hypertension.

EuroInterv ention

13(17) 2069-2076 2018

Kuebler WM, Nicolls MR, Olschewski A, Abe K, Rabinovitch M, Stewart DJ, Chan SY, Morrell NW, Archer SL, Spiekerkoetter E

A Pro - Con debate: Current Controversies in PAH Pathogenesis at the American Thoracic Society International Meeting in 2017.

315(4) L502-L516 2018

Yoshida K, Abe K, Tanaka M, Saku K,

Shinoda-Sakamoto M, Ishikawa T, Watanabe T, Oka M, Sunagawa K, Tsutsui H

Inhibition of

TLR9-NF-kB‒Mediated Sterile Inflammation Improves Pressure Overload‒Induced Right Ventricular Dysfunction in Rats.

Cardiovasc Res.

115(3) 658-668 2019

Nishikawa T, Saku K, Kishi T, Tohyama T, Abe K, Oga Y, Arimura T, Sakamoto T, Yoshida K, Sunagawa K, Tsutsui H

Pulmonary arterial input

impedance reflects the mechanical properties of pulmonary arterial remodeling in rats with pulmonary hypertension.

Life Sci. 212 225-232 2018

Yoshida K, Saku K, Kamada K, Abe K, Tanaka-Ishikawa M, Tohyama T, Nishikawa T, Kishi T, Sunagawa K, Tsutsui H

Electrical Vagal Nerve Stimulation Ameliorates Pulmonary Vascular Remodeling and Improves Survival in Rats With Severe Pulmonary Arterial Hypertension.

JACC Basic Transl Sci.

3(5) 657-671 2018

Kuwabara Y,

Tanaka-Ishikawa M, Abe K, Hirano M, Hirooka Y, Tsutsui H, Sunagawa K, Hirano K

Proteinase-activated Receptor 1 Antagonism Ameliorates Experimental Pulmonary Hypertension.

Cardiovasc Res.

Epub ahead of print

2019

Kawakubo M, Yamasaki Y, Kamitani T, Sagiyama K, Abe K, Hosokawa K, Uabuuchi H, Honda H

Right ventricular area strain with routine cine MRI after balloon pulmonary angioplasty in chronic thromboembolic pulmonary hypertension: Comparison with 2D feature tracking MRI.

Eur Radiol. in press 2019

Abe K, Hosokawa K, Tsutusi H

Traditional Screening Tool in the Era of Modern Treatment for Chronic Thromboembolic Pulmonary Hypertension.

Int J Cardiol.

280 182-183 2019

佐藤徹日本における肺高血圧症診療の

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